호전과 악화를 반복하는 턱밑샘 비대와 양 눈꺼풀 부종으로 내원한 52세 남자
Recurrent Submandibular Mass and Bilateral Periorbital Edema in IgG4-Related Disease: A Case Report
2
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Immunoglobulin G4-related disease (IgG4-RD) is an immune-mediated systemic disorder characterized by inflammatory, proliferative, and fibrotic lesions that can affect any body organ. The severity and extent of organ involvement vary significantly among individuals. Diagnosis of IgG4-RD necessitates a comprehensive assessment, including clinical presentation, radiological findings, laboratory tests, and histopathological examination. The 2019 American College of Rheumatology/ European League Against Rheumatism classification criteria offer a valuable framework for diagnosing IgG4- RD. Although glucocorticoids and rituximab are the primary treatment options, the optimal long-term management strategy for IgG4-RD remains undetermined.
Abstract
Immunoglobulin G4-related disease (IgG4-RD) is an immune-mediated systemic disorder characterized by inflammatory, proliferative, and fibrotic lesions that can affect any body organ. The severity and extent of organ involvement vary significantly among individuals. Diagnosis of IgG4-RD necessitates a comprehensive assessment, including clinical presentation, radiological findings, laboratory tests, and histopathological examination. The 2019 American College of Rheumatology/ European League Against Rheumatism classification criteria offer a valuable framework for diagnosing IgG4- RD. Although glucocorticoids and rituximab are the primary treatment options, the optimal long-term management strategy for IgG4-RD remains undetermined.
참고문헌 (10)
- Perugino CA, "IgG4-related disease : an update on pathophysiology and implications for clinical care", Nat Rev Rheumatol, 16, pp.702~714 (2020)
- Deshpande V, "Consensus statement on the pathology of IgG4-related disease", Mod Pathol, 25, pp.1181~1192 (2012)
- Strehl JD, "Numerous IgG4-positive plasma cells are ubiquitous in diverse localised non-specific chronic inflammatory conditions and need to be distinguished from IgG4-related systemic disorders", J Clin Pathol, 64, pp.237~243 (2011)
- Wallace ZS, "The 2019 American College of Rheumatology", European League Against Rheumatism classification criteria for IgG4-related disease, 2020, pp.72, 7~19
- Kamisawa T, "A new clinicopathological entity of IgG4-related autoimmune disease", J Gastroenterol, 38, pp.982~984 (2003)
- Hamano H, "High serum IgG4concentrations in patients with sclerosing pancreatitis", N Engl J Med, 344, pp.732~738 (2001)
- Katz G, "IgG4-related disease as a variable-vessel vasculitis : a case series of 13 patients with medium-sized coronary artery involvement", Semin Arthritis Rheum, 60, pp.152184~ (2023)
- Katz G, "Proliferative features of IgG4-related disease", Lancet Rheumatol, 6, pp.e481~e492 (2024)
- Khosroshahi A, "International consensus guidance statement on the management and treatment of IgG4-related disease", Arthritis Rheumatol, 67, pp.1688~1699 (2015)
- Della-Torre E, "B-cell depletion works in IgG4-related disease. What else?", Eur J Intern Med, 127, pp.39~40 (2024)