대망에 발생한 IgG4 연관 염증성 가성종양 1예
An IgG4-Related Inflammatory Pseudotumor of the Greater Omentum
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초록
저자들은 자가면역 췌장염이나 경화성 질환의 타 장기의 침범 없이 대망에만 국한되어 발생하였고 악성 종양으로 오인하여 수술적 적출을 시행한 IgG4 연관 염증성 가성종양 1예를 경험하였기에 보고한다. IgG4 연관 염증성 가성종양의 정확한 진단과 치료를 위해서는 IgG4 연관 경화성 질환(IgG4 related sclerosing disease)에 대한 이해와 전신 양전자방출단층촬영(PET-CT)의 해석에 주의가 필요할 것이다.
Abstract
IgG4-related sclerosing disease is a novel clinical disease entity characterized by an elevated serum IgG4 concentration and tissue infiltration by IgG4-positive plasma cells. Although this disease is a novel entity, it is not rare and is present in a proportion of patients with a wide variety of diseases, including autoimmune pancreatitis, sclerosing cholangitis, retroperitoneal fibrosis, and inflammatory pseudotumor. Despite the effectiveness of steroid therapy, IgG4-related sclerosing disease is often misdiagnosed as a malignant tumor. Here, we report an inflammatory pseudotumor of the great omentum that was misdiagnosed as a malignant tumor and subject to surgical resection.
참고문헌 (11)
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