신우 종괴 형성과 췌장 침범을 동반한 IgG4 연관 경화성 질환 1예
A Case of IgG4-Related Pancreas and Kidney Disease Mimicking a Renal Pelvic Malignancy
2
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
IgG4-related sclerosing disease is a disease entity that has recently attracted attention, manifesting as a multiorgan disease characterizedby high serum IgG4 levels, extensive IgG4-positive plasma cells and lymphocyte infiltration of the affected organs, withthe pancreas (autoimmune pancreatitis) and kidney as representative targets. In cases of renal involvement, parenchymal lesions arepredominant, such as renal cortical lesions or diffuse renal enlargement. However, mass-like lesions involving the renal pelvis arevery rare, and mass forming or pelvic involvement types should be distinguished from lymphomas, metastatic cancers and othergenitourinary malignancies to avoid unnecessary surgery. Herein, we report a case of IgG4-related sclerosing disease involving thekidney as an unusual involvement pattern presenting as a mass-like lesion with pelvic and perirenal involvement.
Abstract
IgG4-related sclerosing disease is a disease entity that has recently attracted attention, manifesting as a multiorgan disease characterizedby high serum IgG4 levels, extensive IgG4-positive plasma cells and lymphocyte infiltration of the affected organs, withthe pancreas (autoimmune pancreatitis) and kidney as representative targets. In cases of renal involvement, parenchymal lesions arepredominant, such as renal cortical lesions or diffuse renal enlargement. However, mass-like lesions involving the renal pelvis arevery rare, and mass forming or pelvic involvement types should be distinguished from lymphomas, metastatic cancers and othergenitourinary malignancies to avoid unnecessary surgery. Herein, we report a case of IgG4-related sclerosing disease involving thekidney as an unusual involvement pattern presenting as a mass-like lesion with pelvic and perirenal involvement.
참고문헌 (10)
- Kamisawa T, "A new clinicopathological entity of IgG4-related autoimmune disease", J Gastroenterol, 38, pp.982~984 (2003)
- Khalili K, "Renal cortical lesions in patients with autoimmune pancreatitis: a clue to differentiation from pancreatic malignancy", Eur J Radiol, 67, pp.329~335 (2008)
- Takahashi N, "Renal involvement in patients with autoimmune pancreatitis: CT and MR imaging findings", Radiology, 242, pp.791~801 (2007)
- Vlachou PA, "IgG4-related sclerosing disease: autoimmune pancreatitis and extrapancreatic manifestations", RadioGraphics, 31, pp.1379~1402 (2011)
- 박수정, "자가면역췌장염 55예의 임상 특징, 재발 양상 및 치료 성적", 대한소화기학회지, 52(4), pp.230~246 (2008), 대한소화기학회
- 이유화, "간질성 신염을 동반한 자가면역성 췌장염", 대한내과학회지, 83(6), pp.775~780 (2012), 대한내과학회
- Nishino T, "Clinicopathological differentiation between sclerosing cholangitis with autoimmune pancreatitis and primary sclerosing cholangitis", J Gastroenterol, 42, pp.550~559 (2007)
- Kawano M, "Proposal for diagnostic criteria for IgG4-related kidney disease", Clin Exp Nephrol, 15, pp.615~626 (2011)
- Okazaki K, "Recent advances in the concept and diagnosis of autoimmune pancreatitis and IgG4-related disease", J Gastroenterol, 46, pp.277~288 (2011)
- Kamisawa T, "Research Committee for Intractable Pancreatic Disease and Japan Pancreas Society. Japanese consensus guidelines for management of autoimmune pancreatitis: III. Treatment and prognosis of AIP", J Gastroenterol, 45, pp.471~477 (2010)