고혈압과 성장 부진을 동반한 갈색세포종 2례
Two Cases of Pheochromocytoma Presented with Hypertension and Weight Loss
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초록
갈색세포종은 크롬친화세포에서 분화한 종양으로 소아에서 드문 질환으로 증상을 동반한 동맥성 고혈압을 유발하며 전형적인 증상으로 고혈압, 심계항진, 발한, 두통, 체중감소 등을 보일 수 있다. 이러한 증상을 보이는 고혈압 환아에서 갈색세포종을 의심해보는 것이 필요하며 임상 증상과 생화학 검사로 진단하고 진단시 수술적 절제로 완치 가능한 질환이기에 조기 진단과 절제술이 소아 갈색세포종 치료에 중요하겠다. 고혈압과 성장 부진을 주소로 내원하여 갈색세포종을 진단받고 수술적 절제 후 증상이 호전된 갈색세포종 2예를 보고한다.
Abstract
Pheochromocytoma is a rare disease in children, arising from chromaffin cells of adrenal medullary or extra-adrenal paraganglionic tissues. Typical clinical features include hypertension, diaphoresis, headache, and weight loss. It should therefore be considered that patients associated with hypertension might have pheochromocytoma. The diagnostic approach is based on typical clinical manifestations and biochemical test. Pheochromocytoma is completely curable by surgical resection. Early diagnosis and total excision are the most important aspects of accurate treatment of pheochromocytoma in children. We report two patients with pheochromocytoma presented with hypertension and weight loss both of which were improved after tumor resection.
참고문헌 (20)
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