Isolated Left Ventricular Noncompaction with a Congenital Aneurysm Presenting with Recurrent Embolism
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초록
Isolated left ventricular noncompaction (LVNC) is a rare disorder caused by embryonic arrest of compaction. LVNC is sometimes associated with other congenital cardiac disorders; however, there have been few reports of its coexistence with a left ventricular aneurysm. A 40-year-old woman was admitted to our hospital for renal infarction. She had a history of embolic cerebral infarction 10 years ago. Transthoracic echocardiography showed prominent trabeculae and deep intertrabecular recesses which are filled with blood from the left ventricular (LV) cavity. A thrombus in the akinetic apical wall was confirmed by contrast echocardiography. Using cardiac computed tomography and magnetic resonance imaging, we rejected a possible diagnosis of suspicion of coronary artery disease. She was diagnosed LVNC with a thrombus in apical aneurysm. Here, we report the first patient in Korea known to have LVNC accompanying LV congenital aneurysm presenting with recurrent embolism.
Abstract
Isolated left ventricular noncompaction (LVNC) is a rare disorder caused by embryonic arrest of compaction. LVNC is sometimes associated with other congenital cardiac disorders; however, there have been few reports of its coexistence with a left ventricular aneurysm. A 40-year-old woman was admitted to our hospital for renal infarction. She had a history of embolic cerebral infarction 10 years ago. Transthoracic echocardiography showed prominent trabeculae and deep intertrabecular recesses which are filled with blood from the left ventricular (LV) cavity. A thrombus in the akinetic apical wall was confirmed by contrast echocardiography. Using cardiac computed tomography and magnetic resonance imaging, we rejected a possible diagnosis of suspicion of coronary artery disease. She was diagnosed LVNC with a thrombus in apical aneurysm. Here, we report the first patient in Korea known to have LVNC accompanying LV congenital aneurysm presenting with recurrent embolism.
참고문헌 (15)
- Chin TK, "Isolated noncompaction of left ventricular myocardium. A study of eight cases", Circulation, 82, pp.507~513 (1990)
- Ritter M, "Isolated noncompaction of the myocardium in adults", Mayo Clin Proc, 72, pp.26~31 (1997)
- Burke A, "Left ventricular noncompaction: a pathological study of 14 cases", Hum Pathol, 36, pp.403~411 (2005)
- Ichida F, "Left ventricular noncompaction", Circ J, 73, pp.19~26 (2009)
- Attenhofer Jost CH, "Noncompacted myocardium in Ebstein’s anomaly: initial description in three patients", J Am Soc Echocardiogr, 17, pp.677~680 (2004)
- Betriáan Blasco P, "Ebstein’s anomaly and left ventricular noncompaction association", Int J Cardiol, 119, pp.264~265 (2007)
- Biagini E, "Different types of cardiomyopathy associated with isolated ventricular noncompaction", Am J Cardiol, 98, pp.821~824 (2006)
- Oechslin EN, "Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis", J Am Coll Cardiol, 36, pp.493~500 (2000)
- Oechslin E, "Left ventricular non-compaction revisited: a distinct phenotype with genetic heterogeneity?", Eur Heart J, 32, pp.1446~1456 (2011)
- Sato Y, "Left ventricular aneurysm associated with isolated noncompaction of the ventricular myocardium", Heart Vessels, 21, pp.192~194 (2006)
- Ionescu CN, "Left ventricular noncompaction and aneurysm revealed by left ventriculography" (2011), Catheter Cardiovasc Interv
- Hong Yun, "Isolated Noncompaction of Ventricular Myocardium: a Magnetic Resonance Imaging Study of 11 Patients", Korean Journal of Radiology, 12(6), pp.686~692 (2011), 대한영상의학회
- Maron BJ, "American Heart Association; Council on Clinical Cardiology, Heart Failure and Transplantation Committee; Quality of Care and Outcomes Research and Functional Genomics and Translational Biology Interdisciplinary Working Groups; Council on Epidemiology and Prevention. Contemporary definitions and classification of the cardiomyopathies: an American Heart Association Scientific Statement from the Council on Clinical Cardiology, Heart Failure and Transplantation Committee; Quality of Care and Outcomes Research and Functional Genomics and Translational Biology Interdisciplinary Working Groups; and Council on Epidemiology and Prevention", Circulation, 113, pp.1807~1816 (2006)
- Elliott P, "Classification of the cardiomyopathies: a position statement from the European Society Of Cardiology Working Group on Myocardial and Pericardial Diseases", Eur Heart J, 29, pp.270~276 (2008)
- Jenni R, "Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction: a step towards classification as a distinct cardiomyopathy", Heart, 86, pp.666~671 (2001)