Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?
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The clinical diagnosis of right ventricular (RV) cardiomyopathies is often challenging. It is difficult to differentiate the isolatedleft ventricular (LV) noncompaction cardiomyopathy (NC) from biventricular NC or from coexisting arrhythmogenic ventricularcardiomyopathy (AC). There are currently few established morphologic criteria for the diagnosis other than RV dilation andpresence of excessive regional trabeculation. The gross and microscopic changes suggest pathological similarities between, orcoexistence of, RV-NC and AC. Therefore, the term arrhythmogenic right ventricular cardiomyopathy is somewhat misleading asisolated LV or biventricular involvement may be present and thus a broader term such as AC should be preferred. We describe anunusual case of AC associated with a NC in a 27-year-old man who had a history of permanent pacemaker 7 years ago due tosecond-degree atrioventricular block.
Abstract
The clinical diagnosis of right ventricular (RV) cardiomyopathies is often challenging. It is difficult to differentiate the isolatedleft ventricular (LV) noncompaction cardiomyopathy (NC) from biventricular NC or from coexisting arrhythmogenic ventricularcardiomyopathy (AC). There are currently few established morphologic criteria for the diagnosis other than RV dilation andpresence of excessive regional trabeculation. The gross and microscopic changes suggest pathological similarities between, orcoexistence of, RV-NC and AC. Therefore, the term arrhythmogenic right ventricular cardiomyopathy is somewhat misleading asisolated LV or biventricular involvement may be present and thus a broader term such as AC should be preferred. We describe anunusual case of AC associated with a NC in a 27-year-old man who had a history of permanent pacemaker 7 years ago due tosecond-degree atrioventricular block.
참고문헌 (16)
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