간에서 발생한 고립 섬유종 1예
A Case of Solitary Fibrous Tumor of the Liver
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초록
고립 섬유종은 흉막,1 종격동, 흉선, 상기도 및 이하선2-4 등에 발생하는 중간엽 기원의 종양이다. 1958년 Edmondson이 간의 고립 섬유종을 세계 최초로 기술한 이래5 간실질에서 발생한 예가 매우 드물게 보고되고 있다. 이 종양은 영상 소견이 비특이적이고 양성과 악성의 구별이 어려워 조직검사로 확진이 필요하며 증상 완화의 목적과 악성화의 가능성 때문에 수술 절제가 치료의 근간이 된다.6 본 저자들은 최근 간에서 발생한 고립 섬유종 환자에서 수술 절제 후 완치된 예를 경험하여 이를 문헌 고찰과 함께 국내 최초로 보고하고자 한다.
Abstract
A 46-year-old woman was found to have a huge liver mass that was detected by abdominal ultrasonography. Abdominal CT and MRI showed a 10 cm-sized, encapsulated mass occupying the anterior segment of the right hepatic lobe. Extended right hemihepatectomy was performed and pathological examination revealed fibroblast-like spindle cells within dense deposits of collagen. On immunohistochemical staining, these spindle tumor cells showed an intense CD34 immunoreactivity. The patient is alive without evidence of tumor recurrence 7 months after the resection. Solitary fibrous tumor is a very rare neoplasm found in the liver parenchyma, and it has been reported in less than 30 patients in the English literature. We present here the first such case in Korea.
참고문헌 (17)
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