6세 여아에 발생한 폐 유육종증 1례
A Case of Pulmonary Sarcoidosis in a 6-year-old Girl
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초록
소아에서 유육종증은 드문 질환이지만 본 증례와 같이 급성 호흡부전을 보이는 환아들 중에서 단순 감염성 폐렴으로 오인되어 간과되는 경우가 있을 수도 있다. 따라서 빈호흡과 양측 폐문 림프절 비대를 보이며 예기치 않은 임상경과를 보이는 경우, 폐 유육종증을 감별진단의 범주에 포함시켜 선별검사로서 sACE검사와 그 결과에 따른 조직검사가 필요하다고 제안한다. 저자들은 마이코플라즈마 폐렴으로 오인되었던 6세 여아에서 양측 폐문 림프절 비대, 간효소치 및 sACE치 증가, 스테로이드에 대한 치료반응을 토대로 폐 유육종증으로 진단내린 1례를 문헌고찰과 함께 보고하는 바이다.
Abstract
Sarcoidosis is a rare multisystemic granulomatous disease. The lungs, lymph nodes, eyes, skin and liver are the most commonly involved. There are two distinct forms of sarcoidosis in children. One is early-onset(younger) childhood sarcoidosis characterized by skin rash, uveitis, and arthritis occurring before age 4 years. The other is late-onset(older) childhood sarcoidosis characterized by involvement of the lungs, the common radiographic finding is bilateral hilar lymph node enlargements, similar to the adult manifestation. We report a case of late-onset childhood sarcoidosis in a 6-year-old girl which is the first pediatric pulmonary sarcoidosis reported in Korea.
참고문헌 (18)
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