Focal Dystonia as an Initial Manifestation of Sporadic Creutzfeldt-Jakob Disease with Uncommon MRI Findings
0
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Sporadic Creutzfeldt-Jakob disease (CJD) is a rare progressive spongiform encephalopathy. Involuntary movements commonly occur in the course of sporadic CJD, but focal dystonia alone as an initial manifestation is rare. We described a 40-yr-old man who presented with a 2 week history of focal dystonia in the neck and left arm. Interestingly, diffusion-weighted images revealed high signal intensities in the right temporal, posterior parietal, and occipital cortices rather than in the striatum.
Abstract
Sporadic Creutzfeldt-Jakob disease (CJD) is a rare progressive spongiform encephalopathy. Involuntary movements commonly occur in the course of sporadic CJD, but focal dystonia alone as an initial manifestation is rare. We described a 40-yr-old man who presented with a 2 week history of focal dystonia in the neck and left arm. Interestingly, diffusion-weighted images revealed high signal intensities in the right temporal, posterior parietal, and occipital cortices rather than in the striatum.
참고문헌 (13)
- Malte^te D, "Movement disorders and Creutzfeldt-Jakob disease: a review", Parkinsonism Relat Disord, 12, pp.65~71 (2006)
- Johnson RT, "Creutzfeldt-Jakob disease and related transmissible spongiform encephalopathies", N Engl J Med, 339, pp.1994~2004 (1998)
- Brown P, "Creutzfeldt-Jakob disease: clinical analysis of a consecutive series of 230 neuropathologically verified cases", Ann Neurol, 20, pp.597~602 (1986)
- Will RG, "A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970-79. I: Clinical features", J Neurol Neurosurg Psychiatry, 47, pp.134~140 (1984)
- Edler J, "Movement disturbances in the differential diagnosis of Creutzfeldt- Jakob disease", Mov Disord, 24, pp.350~356 (2009)
- Will RG, "A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970-1979. II: Epidemiology", J Neurol Neurosurg Psychiatry, 49, pp.749~755 (1986)
- Lee SH, "Spreading dystonia in probable Creutzfeldt- Jakob disease with serial diffusion-weighted magnetic resonance images", Eur Neurol, 58, pp.122~124 (2007)
- Hellmann MA, "Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease", Mov Disord, 17, pp.1097~1098 (2002)
- Malte^te D, "Hemidystonia as initial manifestation of sporadic Creutzfeldt-Jakob disease", Eur J Neurol, 13, pp.667~668 (2006)
- Sethi KD, "Creutzfeldt-Jakob’s disease presenting with ataxia and a movement disorder", Mov Disord, 6, pp.157~162 (1991)
- Zochodne DW, "Creutzfeldt-Jakob disease without periodic sharp wave complexes: a clinical, electroencephalographic, and pathologic study", Neurology, 38, pp.1056~1060 (1988)
- Tschampa HJ, "Radiological assessment of Creutzfeldt- Jakob disease", Eur Radiol, 17, pp.1200~1211 (2007)
- Ridding MC, "Changes in the balance between motor cortical excitement and inhibition in focal, task specific dystonia", J Neurol Neurosurg Psychiatry, 59, pp.493~498 (1995)