본문 바로가기
KERD
논문KCI 등재

뒤시엔느형 근디스트로피 환자의 심장기능 평가

The Evaluation of Cardiac Function in Duchenne Muscular Dystrophy

임상희|강성웅|문재호|허현석|박사윤
대한재활의학회 (Korean Academy Of Rehabilitation Medicine)|2004.12|Annals of Rehabilitation Medicine|제28권 제6호|pp. 559-564

3

조회

0

다운로드

1

인용

0

참고문헌

주제분류재활의학

초록

Abstract

Objective: To evaluate the cardiac function and to explore the importance of the evaluation of cardiac function in patients with Duchenne muscular dystrophy (DMD). Method: Thirty-nine patients with DMD without any symptoms of heart problems underwent physical examinations and cardiac monitoring including the arterial carbon dioxide (CO2) screening. Thirty one patients underwent pulmonary function test. Results: Among 39 patients 27 showed abnormal electrocardiographic findings such as ventricular hypertrophy, ischemic change, atrial hypertrophy, T wave inversion, sinus tachycardia and ST elevation. 24 patients showed abnormal echocardiographic findings such as abnormal ejection fraction, dilated cardiomyopathy (DCMP), filling abnormality of left ventricle, global hypokinesia and reduced systolic function. 17 patients showed low ejection fraction (below 59%) and 4 of them were diagnosed as DCMP. There were significant correlations between age and ejection fraction (r=-0.552, p＜0.01), between functional level and ejection fraction (r=-0.607, p＜0.01) and between vital capacity and ejection fraction (r=0.547, p＜0.01). However, ejection fraction showed no significant correlations with arterial CO2. Conclusion: Routine evaluation of the cardiac function, at least from 10 years of age, and proper treatment following early diagnosis of heart problems were necessary in patients with DMD, because they possibly have been severely affected by cardiac problems without any clinical symptoms.

참고문헌 (22)

  1. "뒤시엔느형 근디스트로피 환자의 포괄적 임상 고찰", 24, pp.241~248 (2001)
  2. "Conventional approaches to managing neuromuscular ventilatory failure. In", pp.285~301 (1996), Hanley & Belfus
  3. "Update and perspectives on noninvasive respiratory muscle aids:part 1-the inspiratory muscle aids", 105, pp.1230~1240 (1994)
  4. "Update and perspectives on noninvasive respiratory muscle aids:part 2-the expiratory muscle aids", 105, pp.1538~1544 (1994)
  5. "Prevention of pulmonary morbidity for patients with Duchenne muscular dystrophy", 112, pp.1204~1208 (1997)
  6. "Management of end stage respiratory failure in Duchenne muscular dystrophy", 10, pp.177~182 (1987)
  7. "The heart in Duchenne muscular dystrophy", pp.1239~1244
  8. "Normal and abnormal myocardial function. In", pp.1309~1310 (2001), McGraw Hill
  9. "Systolic time intervals in Duchenne muscular dystrophy:Evaluation of left ventricular performance", 11, pp.407~411 (1988)
  10. "Cardiomyopathy of Duchenne muscular dystrophy", 9, pp.205~213 (1988)
  11. "The pathologic findings in heart muscle in progressive muscular dystrophy", 9, pp.59~72 (1923)
  12. "Sequence of cardiac changes in Duchenne muscular dystrophy", 95, pp.283~294 (1978)
  13. "Cardiovascular considerations in the management of neuromuscular disease", 15, pp.93~108 (1995)
  14. "A management trial for Duchenne cardiomyopathy", 74, pp.345~350 (1995)
  15. "Evaluation of myocardial involvement in Duchenne's progressive muscular dystrophy with thallium-201 myocardial perfusion imaging", 26, pp.767~777 (1985)
  16. "The incidence and evolution of cardiomyopathy in Duchenne muscular dystrophy", 26, pp.271~277 (1990)
  17. "Neuroendocrine changes in chronic cardiac failure", 91, pp.13~20 (1996)
  18. "Prolongation of life in Duchenne muscular dystrophy", pp.118~124 (1983)
  19. "Systolic time interval characteristics in children with Duchenne's progressive muscular dystrophy", 70, pp.985~964 (1982)
  20. "Gated radionuclide ventriculography in the evaluation of cardiac function in Duchenne's muscular dystrophy", 94, pp.1245~1248
  21. "Gradients of functional ability of importance in rehabilitation of patients with progressive muscular and neuromuscular disease", 38, pp.574~579 (1957)
  22. "Evaluation of myocardial damage in Duchenne's muscular dystrophy with thallium-201 myocardial SPECT", ya(k), pp.51~61

관련 논문AI추천

듀센형 근이영양증 환자에서의 심장 침범의 양상강성웅, 권력문, 권성우, 김현승, 김혜진, 문재연, 박종관, 박찬익, 윤영원, 이성주, 이지혁, 임세중, 홍범기한국심초음파학회 · Journal of Cardiovascular Imaging2005 · 제13권 제4호뒤시엔느형 근디스트로피 환자의 포괄적 임상고찰강성웅, 김윤진, 나영무, 문재호, 박윤길, 박준수대한재활의학회 · Annals of Rehabilitation Medicine2001 · 제25권 제2호확장형심근병증과 뇌경색증을 동반한 듀센 근육이영양증 환자김선정, 서경임, 송태진, 이명준, 이준범, 조한나, 최영철대한신경과학회 · 대한신경과학회지2009 · 제27권 제1호Muscle Pathology Associated With Cardiac Function in Duchenne Muscular DystrophyKim, Soo-Yeon, Lee Byeong-Ju, Lee Heirim, Lee In Sook, Shin Yong Beom, Song You Seon, Yoon Jin A대한재활의학회 · Annals of Rehabilitation Medicine2024 · 제48권 제6호듀시엔형 근이영양증과 베커 근이영양증 환자의 심장 기능 평가송태진, 최영철대한신경과학회 · 대한신경과학회지2007 · 제25권 제4호Early Marker of Myocardial Deformation in Children with Duchenne Muscular Dystrophy Assessed Using Echocardiographic Myocardial Strain Analysis강성웅, 은영민, 정조원, 조원하, 최재영연세대학교의과대학 · Yonsei Medical Journal2016 · 제57권 제4호

이 간행물의 다른 논문 (12건)

뇌졸중 환자에서 시각적 바이오피드백을 이용한 균형 훈련 효과김연희, 우영근, 신재은, 김두환, 김남균pp. 515-522뇌손상 장애인의 운전을 위한 인지-지각능력 평가 도구의 개발과 적용: '운전자 인지행동검사'와의 비교장순자, 김선일, 이준욱, 정원국, 이장한, 유정헌, 김동아, 박시운pp. 523-531팔걸이가 편마비 환자의 기립자세 균형에 미치는 영향한승진, 윤성익, 이규훈, 김미정, 이도경pp. 532-536성인 뇌성마비에서 보행시 에너지 소모량 평가박은숙, 박창일, 장현정, 조성래pp. 537-541뇌성마비아 족부 변형의 방사선 평가김세주, 송은범pp. 549-558
원문 보기