Successful Surgery for Scoliosis Supported by Pulmonary Rehabilitation in a Duchenne Muscular Dystrophy Patient With Forced Vital Capacity Below 10%
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Low vital capacity is a risk factor for scoliosis correction operation in Duchenne muscular dystrophy (DMD) patients, but pulmonary rehabilitation, including noninvasive intermittent positive pressure ventilator application, air stacking exercise, and assisted coughing technique, reduces the pulmonary complications and perioperative mortality risk. In this case, the patient’s preoperative forced vital capacity (FVC) was 8.6% of normal predicted value in sitting position and 9.4% in supine position. He started pulmonary rehabilitation before the operation and continued right after the operation. Scoliosis correction operation was successful without any pulmonary complications, and his discomfort in sitting position was improved. If pulmonary rehabilitative support is provided properly, FVC below 10% of normal predicted value is not a contraindication of scoliosis correction operation in DMD patients.
Abstract
Low vital capacity is a risk factor for scoliosis correction operation in Duchenne muscular dystrophy (DMD) patients, but pulmonary rehabilitation, including noninvasive intermittent positive pressure ventilator application, air stacking exercise, and assisted coughing technique, reduces the pulmonary complications and perioperative mortality risk. In this case, the patient’s preoperative forced vital capacity (FVC) was 8.6% of normal predicted value in sitting position and 9.4% in supine position. He started pulmonary rehabilitation before the operation and continued right after the operation. Scoliosis correction operation was successful without any pulmonary complications, and his discomfort in sitting position was improved. If pulmonary rehabilitative support is provided properly, FVC below 10% of normal predicted value is not a contraindication of scoliosis correction operation in DMD patients.
참고문헌 (10)
- Rawlins BA., "Reconstructive spine surgery in pediatric patients with major loss in vital capacity", J Pediatr Orthop, 16, pp.284~292 (1996)
- 강성웅, "Pulmonary Rehabilitation in Patients with Neuromuscular Disease", Yonsei Medical Journal, 47(3), pp.307~314 (2006), 연세대학교의과대학
- Takaso M., "Surgical management of severe scoliosis with high risk pulmonary dysfunction in Duchenne muscular dystrophy : patient function, quality of life and satisfaction", Int Orthop, 34, pp.695~702 (2010)
- Gill I., "Correction of neuromuscular scoliosis in patients with preexisting respiratory failure", Spine (Phila Pa 1976), 31, pp.2478~2483 (2006)
- Cheuk DK., "Surgery for scoliosis in Duchenne muscular dystrophy", Cochrane Database Syst Rev, (1), pp.CD005375~ (2007)
- Larsson EL., "Longterm follow-up of functioning after spinal surgery in patients with neuromuscular scoliosis", Spine(Phila Pa 1976), 30, pp.2145~2152 (2005)
- Master DL., "Risk factors for major complications after surgery for neuromuscular scoliosis", Spine(Phila Pa 1976), 36, pp.564~571 (2011)
- Sussman MD., "Advantage of early spinal stabilization and fusion in patients with Duchenne muscular dystrophy", J Pediatr Orthop, 4, pp.532~537 (1984)
- Yamashita T., "Correlation between progression of spinal deformity and pulmonary function in Duchenne muscular dystrophy", J Pediatr Orthop, 21, pp.113~116 (2001)
- 강성웅, "신경근육계 질환에서 공기누적운동의 임상적 의의", Annals of Rehabilitation Medicine, 31(3), pp.346~350 (2007), 대한재활의학회