Arnold-Chiari Malformation Type III With Meningoencephalocele: A Case Report
1
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Arnold-Chiari malformation type III (CM III) is an extremely rare anomaly with poor prognosis. An encephalocele with brain anomalies as seen in CM II, and herniation of posterior fossa contents like the cerebellum are found in CM III. The female infant was a twin, born at 33 weeks, weighing 1.7 kg with a huge hydrocele on the craniocervical junction. After operations were performed, she was referred to the department of rehabilitation medicine for poor motor development, swallowing dysfunction, and poor eye fixation at 22 months. The child was managed with neurodevelopmental treatment, oromotor facilitation, and light perception training. After 14 months, improvement of gross motor function was observed, including more stable head control, rolling, and improvement of visual perception. CM III has been known as a condition with poor prognosis. However, with the improvement in operative techniques and intensive rehabilitations, the prognosis is more promising than ever before. Therefore, more attention must be paid to the rehabilitation issues concerning patients with CM III.
Abstract
Arnold-Chiari malformation type III (CM III) is an extremely rare anomaly with poor prognosis. An encephalocele with brain anomalies as seen in CM II, and herniation of posterior fossa contents like the cerebellum are found in CM III. The female infant was a twin, born at 33 weeks, weighing 1.7 kg with a huge hydrocele on the craniocervical junction. After operations were performed, she was referred to the department of rehabilitation medicine for poor motor development, swallowing dysfunction, and poor eye fixation at 22 months. The child was managed with neurodevelopmental treatment, oromotor facilitation, and light perception training. After 14 months, improvement of gross motor function was observed, including more stable head control, rolling, and improvement of visual perception. CM III has been known as a condition with poor prognosis. However, with the improvement in operative techniques and intensive rehabilitations, the prognosis is more promising than ever before. Therefore, more attention must be paid to the rehabilitation issues concerning patients with CM III.
참고문헌 (10)
- Chiari H, "Concerning alterations in the cerebellum resulting from cerebral hydrocephalus", Pediatr Neurosci, 13, pp.3~8 (1987)
- Cama A, "Chiari complex in children: neuroradiological diagnosis, neurosurgical treatment and proposal of a new classification (312 cases)", Eur J Pediatr Surg, 5(Suppl 1), pp.35~38 (1995)
- Castillo M, "Chiari III malformation:imaging features", AJNR Am J Neuroradiol, 13, pp.107~113 (1992)
- Cho EY, "A case of Chiari III malformation", J Korean Child Neurol Soc, 13, pp.282~287 (2005)
- Hoyt CS, "Visual function in the brain-damaged child", Eye (Lond), 17, pp.369~384 (2003)
- Laget P, "Maturation of visually evoked potentials in the normal child", Electroencephalogr Clin Neurophysiol, 43, pp.732~744 (1977)
- Dutton GN, "Cerebral visual impairment in children", Semin Neonatol, 6, pp.477~485 (2001)
- Malkowicz DE, "Rehabilitation of cortical visual impairment in children", Int J Neurosci, 116, pp.1015~1033 (2006)
- McLone DG, "The cause of Chiari II malformation: a unified theory", Pediatr Neurosci, 15, pp.1~12 (1989)
- Snyder WE Jr, "Chiari III malformation treated with CSF diversion and delayed surgical closure", Pediatr Neurosurg, 29, pp.117~120 (1998)