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혈액 투석 환자에서 발생한 경화성 피막성 복막염 1예

Encapsulating Peritoneal Sclerosis Occurring in a Hemodialysis Patient

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초록

저자들은 B형 간염에 의한 간경화가 있는 혈액투석 환자에서 반복적인 복수 및 복막염의 증상이 발생하여 경화성 복막염 의심하에 개복술로 이를 확진하였고 이후 스테로이드 치료로 호전된 경화성 피막성 복막염을 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Abstract

Encapsulating peritoneal fibrosis (EPF) is a serious, uncommon complication of chronic peritoneal dialysis. However, it is rare in hemodialysis patients. EPF is characterized by peritoneal membrane inflammation followed by peritoneal membrane fibrosis and encapsulation. The etiology is unclear, but inflammation of the deteriorated peritoneum causes peritoneal fibrosis. We present a case of EPF that occurred in a 29-year-old man with hepatitis B-associated liver cirrhosis with ascites that was treated solely with hemodialysis. We managed this patient surgically and then medically with prednisolone. To our knowledge, this is the first such case in Korea, so we report this case with a literature review.

참고문헌 (10)

  1. Gandhi VC, "Sclerotic thickening of the peritoneal membrane in maintenance peritoneal dialysis patients", Arch Intern Med, 140, pp.1201~1203 (1980)
  2. Kawaguchi Y, "Encapsulating peritoneal sclerosis: definition, etiology, diagnosis, and treatment: International Society for Peritoneal Dialysis Ad Hoc Committee on Ultrafiltration Management in Peritoneal Dialysis", Perit Dial Int, 20(4), pp.43~55 (2000)
  3. McLaughlin K, "Sclerosing peritonitis occurring in a hemodialysis patient", Am J Kidney Dis, 27, pp.729~732 (1996)
  4. 정지윤, "타목시펜과 프레드니솔론으로 호전된 경화성 피막성 복막염 (sclerosing encapsulating peritonitis)", Kidney Research and Clinical Practice, 28(6), pp.685~692 (2009), 대한신장학회
  5. Kawanishi H, "Encapsulating peritoneal sclerosis-like findings in a hemodialysis patient without a history of peritoneal dialysis", Adv Perit Dial, 19, pp.176~179 (2003)
  6. Guest S, "Tamoxifen therapy for encapsulating peritoneal sclerosis : mechanism of action and update on clinical experiences", Perit Dial Int, 29, pp.252~255 (2009)
  7. Won Na Suh, "Sclerosing Encapsulating Peritonitis (Abdominal Cocoon) after Abdominal Hysterectomy", The Korean Journal of Internal Medicine, 22(2), pp.125~129 (2007), 대한내과학회
  8. Naiki Y, "Involvement of TGFbeta signal for peritoneal sclerosing in continuous ambulatory peritoneal dialysis", J Nephrol, 16, pp.95~102 (2003)
  9. Mege JL, "Monocyte production of transforming growth factor beta in long-term hemodialysis : modulation by hemodialysis membranes", Am J Kidney Dis, 28, pp.395~399 (1996)
  10. Kawanishi H, "Experience of 100 surgical cases of encapsulating peritoneal sclerosis : investigation of recurrent cases after surgery", Adv Perit Dial, 22, pp.60~64 (2006)

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