림프절외 변연부 B-세포 림프종과 동반된 루프스양사구체신염 1예
Lupus-like Glomerulonephritis Associated with Extranodal Marginal Zone B-cell Lymphoma of MALT Eui
0
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
이 증례에서 저자들은 전신부종으로 내원한 49세 남환에서 루프스양사구체신염을 동반한 림프절외 변연부 B-세포림프종을 진단하였고 항암화학요법으로 치료한 증례를 경험하였다. 현재까지 루프스양사구체신염의 발병 기전, 원인, 치료, 예후에 대해 잘 알려지진 않았으나, 이 질환이 진단된 경우 적극적으로 원인질환을 평가하고 조기에 적절히 치료하는 것이 신장의 예후에 있어서 중요할 것으로 생각된다.
Abstract
Lupus-like glomerulonephritis is an immune complex disease with features of lupus nephritis in the absence of systemic lupus erythematosus (SLE). We report a 49-year-old man diagnosed with lupus-like glomerulonephritis associated with extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue (MALT). He was admitted to the hospital for edema. At admission, the serum creatinine was 2.2 mg/dL and the urine protein level was 3.9 mg/day. A renal biopsy showed features of lupus nephritis with no clinical or serological evidence of SLE. Extranodal marginal zone B-cell lymphoma of MALT was discovered concurrently. After successful chemotherapy, the lupus-like glomerulonephritis and lymphoma entered complete remission.
참고문헌 (12)
- Huerta A, "Renal-limited ‘lupus-like’ nephritis", Nephrol Dial Transplant, 27, pp.2337~2342 (2012)
- Pirkle JL, "Immune complex disease with a lupus-like pattern of deposition in an antinuclear antibody-negative patient", Am J Kidney Dis, 62, pp.159~164 (2013)
- Sobh MA, "Schistosomal specific nephropathy leading to end-stage renal failure", Kidney Int, 31, pp.1006~1011 (1987)
- Haas M, "HIV-associated immune complex glomerulonephritis with"lupus-like"features : a clinicopathologic study of 14 cases", Kidney Int, 67, pp.1381~1390 (2005)
- Silva H, "Renal involvement in active juvenile’ cirrhosis", J Clin Pathol, 18, pp.157~163 (1965)
- Shimizu K, "Primary thymic mucosa-associated lymphoid tissue lymphoma : diagnostic tips", J Thorac Oncol, 5, pp.117~121 (2010)
- Doi H, "Primary hepatic marginal zone B cell lymphoma of mucosa-associated lymphoid tissue type : case report and review of the literature", Int J Hematol, 88, pp.418~423 (2008)
- Adamidis KN, "Splenic marginal lymphoma and glomerulonephritis : case report and review of the literature", Ren Fail, 32, pp.281~285 (2010)
- Weening JJ, "The classification of glomerulonephritis in systemic lupus erythematosus revisited", Kidney Int, 65, pp.521~530 (2004)
- Lech M, "The pathogenesis of lupus nephritis", J Am Soc Nephrol, 24, pp.1357~1366 (2013)
- Yeo SC, "An unusual case of glomerulonephritis in a patient with non-Hodgkin mucosal associated lymphoid tissue(MALT)B-cell lymphoma", BMC Nephrol, 14, pp.158~ (2013)
- Matignon M, "A lupus-like glomerulonephritis following acute HIV-1seroconversion in an African woman", Nephrol Dial Transplant, 20, pp.438~440 (2005)