안면상완근긴장발작으로 발현한 항LGI1항체 자가면역뇌염
Anti-LGI1 Antibody Autoimmune Encephalitis Which Manifests Faciobrachial Dystonic Seizure
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초록
Anti-LGI1 (leucine-rich glioma inactivated-1) antibody encephalitis is one of autoimmune encephalitis. We report a66-year-old man who presented with frequent, brief dystonic seizures which involve predominantly ipsilateral face andarm without cognitive impairment. Brain MRI showed normal finding. Serum and CSF tests revealed anti-LGI1antibody. His symptom was not relieved by antiepileptic drugs, but completely controlled after immunotherapy. Thiscase indicates that recognition of the brief, dystonic seizures should do tests for anti-LGI1 antibodies.
Abstract
Anti-LGI1 (leucine-rich glioma inactivated-1) antibody encephalitis is one of autoimmune encephalitis. We report a66-year-old man who presented with frequent, brief dystonic seizures which involve predominantly ipsilateral face andarm without cognitive impairment. Brain MRI showed normal finding. Serum and CSF tests revealed anti-LGI1antibody. His symptom was not relieved by antiepileptic drugs, but completely controlled after immunotherapy. Thiscase indicates that recognition of the brief, dystonic seizures should do tests for anti-LGI1 antibodies.
참고문헌 (10)
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