발작성야간혈색뇨증과 동반된 진행성 모야모야증후군
Progressive Moyamoya Syndrome Associated with Paroxysmal Nocturnal Hemoglobinuria
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A 31-year-old female with paroxysmal nocturnal hemoglobinuria (PNH) presented with left hemiparesis. One year priorto this presentation she had been diagnosed with bihemispheric cerebral infarctions associated with moyamoyasyndrome. During her current presentation, MRI revealed acute infarction of the right hemisphere and MRA revealedocclusion of the right internal carotid artery (ICA), and aggravation of the preexisting stenosis of the contralateral ICAand ipsilateral posterior cerebral artery compared to the previous MRA. We report herein a case of progressivemoyamoya syndrome associated with PNH.
Abstract
A 31-year-old female with paroxysmal nocturnal hemoglobinuria (PNH) presented with left hemiparesis. One year priorto this presentation she had been diagnosed with bihemispheric cerebral infarctions associated with moyamoyasyndrome. During her current presentation, MRI revealed acute infarction of the right hemisphere and MRA revealedocclusion of the right internal carotid artery (ICA), and aggravation of the preexisting stenosis of the contralateral ICAand ipsilateral posterior cerebral artery compared to the previous MRA. We report herein a case of progressivemoyamoya syndrome associated with PNH.
참고문헌 (10)
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