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봉입소체근염의 증례를 통한 임상, 병리학적, 혈청학 고찰

A Case of Inclusion Body Myositis with Clinical, Pathological and Serological Consideration

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초록

Inclusion body myositis is a rare condition of idiopathic inflammatory myopathy. Prior criteria for the diagnosis of inclusion body myositis essentially required pathological features of rimmed vacuoles, tubulofilamentous inclusions, and amyloid deposits. However, recently developed new diagnostic criteria emphasize clinical characteristics including weakness of finger flexors and knee extensors. In addition, a serological evaluation of anti-cN1A antibody is helpful for the diagnosis. We report a case of inclusion body myositis with clinical, pathological, and serological consideration.

Abstract

Inclusion body myositis is a rare condition of idiopathic inflammatory myopathy. Prior criteria for the diagnosis of inclusion body myositis essentially required pathological features of rimmed vacuoles, tubulofilamentous inclusions, and amyloid deposits. However, recently developed new diagnostic criteria emphasize clinical characteristics including weakness of finger flexors and knee extensors. In addition, a serological evaluation of anti-cN1A antibody is helpful for the diagnosis. We report a case of inclusion body myositis with clinical, pathological, and serological consideration.

참고문헌 (10)

  1. Greenberg SA, "Inclusion body myositis : clinical features and pathogenesis", Nat Rev Rheumatol, 15, pp.257~272 (2019)
  2. Griggs RC, "Inclusion body myositis and myopathies", Ann Neurol, 38, pp.705~713 (1995)
  3. Rose MR, "188th ENMC International Workshop : inclusion body myositis, 2-4 December 2011, Naarden, The Netherlands", Neuromuscul Disord, 23, pp.1044~1055 (2013)
  4. Tanboon J, "Classification of idiopathic inflammatory myopathies : pathology perspectives", Curr Opin Neurol, 32, pp.704~714 (2019)
  5. 박영은, "주요 근육병리 소견을 바탕으로 한 근육병의 진단", 대한신경과학회지, 39(4), pp.274~286 (2021), 대한신경과학회[DOI]
  6. Mavroudis I, "Diagnostic accuracy of anti-cN1A on the diagnosis of inclusion body myositis. a hierarchical Bivariate and Bayesian metaanalysis", J Clin Neuromuscul Dis, 23, pp.31~38 (2021)
  7. Tawara N, "Pathomechanisms of anti-cytosolic 5’-nucleotidase 1A autoantibodies in sporadic inclusion body myositis", Ann Neurol, 81, pp.512~525 (2017)
  8. Lucchini M, "Anti-cN1A antibodies are associated with more severe dysphagia in sporadic inclusion body myositis", Cells, 10, pp.1146~ (2021)
  9. Paul P, "Anti-cN1A antibodies do not correlate with specific clinical, electromyographic, or pathological findings in sporadic inclusion body myositis", Muscle Nerve, 63, pp.490~496 (2021)
  10. Felice KJ, "Sensitivity and clinical utility of the anti-cytosolic 5’-nucleotidase 1A(cN1A)antibody test in sporadic inclusion body myositis : report of 40 patients from a single neuromuscular center", Neuromuscul Disord, 28, pp.660~664 (2018)

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