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Primitive Myxoid Mesenchymal Tumor of Infancy: A Case Report
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Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare malignant tumor that oc-curs in the soft tissue in early childhood. This malignant tumor can occur in various parts ofthe body, such as the trunk, extremity, and head & neck area, and is characterized by aggres-sive local infiltration. There is no standardized treatment so far because this tumor is very rareworldwide. Still now, the principle of treatment so far is complete surgical resection. We per-formed a surgical treatment for a 3-year-old PMMTI patient who visited the hospital with anincidentally discovered mass in the posterior neck. If surgical treatment is selected as thetreatment for PMMTI, it is thought that resection with sufficient margins during surgery willhelp reduce recurrence. In addition, since local recurrence is frequent and the average recur-rence-free duration is short, careful short-term follow-up is necessary.
Abstract
Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare malignant tumor that oc-curs in the soft tissue in early childhood. This malignant tumor can occur in various parts ofthe body, such as the trunk, extremity, and head & neck area, and is characterized by aggres-sive local infiltration. There is no standardized treatment so far because this tumor is very rareworldwide. Still now, the principle of treatment so far is complete surgical resection. We per-formed a surgical treatment for a 3-year-old PMMTI patient who visited the hospital with anincidentally discovered mass in the posterior neck. If surgical treatment is selected as thetreatment for PMMTI, it is thought that resection with sufficient margins during surgery willhelp reduce recurrence. In addition, since local recurrence is frequent and the average recur-rence-free duration is short, careful short-term follow-up is necessary.
참고문헌 (14)
- Alaggio R, "Primitive myxoid mesenchymal tumor of infancy : A clinicopathologic report of 6cases", Am J Surg Pathol, 30(3), pp.388~394 (2006)
- Haga M, "Primitive myxoid mesenchymal tumor of infancy with fatal hemorrhage in utero : A case report and literature review", J Pediatr Hematol Oncol, 45(1), pp.e135~8 (2023)
- Gong Q, "Primitive myxoid mesenchymal tumor of infancy : Report of two cases and review of the literature", Pathol Int, 62(8), pp.549~553 (2012)
- Asaftei SD, "Management of unresectable metastatic primitive myxoid mesenchymal tumor of infancy : A case report and systematic review of the literature", J Pediatr Hematol Oncol, 42(3), pp.163~169 (2020)
- Guilbert MC, "Transformation of a primitive myxoid mesenchymal tumor of infancy to an undifferentiated sarcoma : A first reported case", J Pediatr Hematol Oncol, 37(2), pp.e118~20 (2015)
- Mulligan L, "Primitive myxoid mesenchymal tumor of infancy : A report of a further case with locally aggressive behavior", Pediatr Dev Pathol, 14(1), pp.75~79 (2011)
- Cramer SL, "Successful treatment of recurrent primitive myxoid mesenchymal tumor of infancy with BCOR internal tandem duplication", J Natl Compr Canc Netw, 15(7), pp.868~871 (2017)
- Saeed AA, "Primitive myxoid mesenchymal tumor of infancy with brain metastasis : First reported case", Childs Nerv Syst, 35(2), pp.363~368 (2019)
- Cuthbertson DW, "A cooperative approach to diagnosis of rare diseases : Primitive myxoid mesenchymal tumor of infancy", Ann Clin Lab Sci, 44(3), pp.310~316 (2014)
- Memmott T, "Combination therapy for unresectable primitive myxoid mesenchymal tumor of infancy : A story of cure", Pediatr Blood Cancer, 69(7), pp.e29523~ (2022)
- Lam J, "Primitive myxoid mesenchymal tumor of infancy in a preterm infant", Pediatr Dermatol, 27(6), pp.635~637 (2010)
- Su TC, "A rare malignant tumor of scalp in a 3-month-old Taiwanese infancy : Case report of primitive myxoid mesenchymal tumor of infancy with molecular study", Med Mol Morphol, 46(2), pp.109~113 (2013)
- Saito A, "A case with sacrococcygeal primitive myxoid mesenchymal tumor of infancy : A case report and review of the literature", J Pediatr Hematol Oncol, 35(7), pp.e280~2 (2013)
- Cipriani NA, "Primitive myxoid mesenchymal tumor of infancy with rosettes : A new finding and literature review", Int J Surg Pathol, 22(7), pp.647~651 (2014)