비부비동내에서 발생한 원발성 Ewing씨 육종 1예
A Case of Primary Ewing’s Sarcoma of Arising from the Nasal Cavity
1
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Ewing’s sarcoma is an uncommon malignancy that usually occurs in children. It most commonly involves the lower extremity, with the pelvis being the next most common site. Primary Ewing’s sarcoma that arises in the head and neck region is extremely rare, representing only 1-4% of all Ewing’s sarcoma cases. We report a case of primary Ewing’s sarcoma in the nasal cavity in a 10-year old patient with a non-specific past medical history, in which the patient received 3 trials of neoadjuvant chemotherapy, endoscopic wide excision, followed by 2 more trials of adjuvant chemotherapy. Currently, it has been 5 years since treatment and the patient did not exhibit any signs or symptoms of recurrence of the disease.
Abstract
Ewing’s sarcoma is an uncommon malignancy that usually occurs in children. It most commonly involves the lower extremity, with the pelvis being the next most common site. Primary Ewing’s sarcoma that arises in the head and neck region is extremely rare, representing only 1-4% of all Ewing’s sarcoma cases. We report a case of primary Ewing’s sarcoma in the nasal cavity in a 10-year old patient with a non-specific past medical history, in which the patient received 3 trials of neoadjuvant chemotherapy, endoscopic wide excision, followed by 2 more trials of adjuvant chemotherapy. Currently, it has been 5 years since treatment and the patient did not exhibit any signs or symptoms of recurrence of the disease.
참고문헌 (11)
- Som PM, "Ewing’s sarcoma of the mandible", Ann Otol Rhinol Laryngol, 89(1 Pt 1), pp.20~23 (1980)
- Crowe WW, "Ewing’s sarcoma with primary lesion in mandible: report of case", J Oral Surg, 23, pp.156~162 (1965)
- Watanabe H, "Primary Ewing’s sarcoma of the temporal bone", Surg Neurol, 37(1), pp.54~58 (1992)
- Kim HK, "A case of Ewing’s sarcoma arising in the Lt. Mandible", Korean J Otolaryngol-Head Neck Surg, 26(1), pp.187~192 (1983)
- Balamuth NJ, "Ewing’s sarcoma", Lancet Oncol, 11(2), pp.184~192 (2010)
- Grier HE, "Ewing family of tumors. Ewing’s sarcoma and primitive neuroectodermal tumors", Pediatr Clin North Am, 44(4), pp.991~1004 (1997)
- Delattre O, "Gene fusion with an ETS DNA-binding domain caused by chromosome translocation in human tumours", Nature, 359(6391), pp.162~165 (1992)
- Koh JW, "Primary Ewing’s sarcoma arising from the mandible: a case report", Korean J Otolaryngol-Head Neck Surg, 42(2), pp.249~254 (1999)
- Bacchini P, "Ewing’s sarcoma of the mandible and maxilla. A report of three cases from the Istituto Beretta", Oral Surg Oral Med Oral Pathol, 61(3), pp.278~283 (1986)
- 이성부, "비·부비동 육종의 치료 결과: 서울아산병원의 치료 경험 20예", 대한이비인후과학회지 두경부외과학, 52(7), pp.579~584 (2009), 대한이비인후과학회
- Jaffe N, "Improved outlook for Ewing’s sarcoma with combination chemotherapy (vincristine, actinomycin D and cyclophosphamide) and radiation therapy", Cancer, 38(5), pp.1925~1930 (1976)