A Case with Bibrachial Variant of Guillain-Barré Syndrome
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The bibrachial variant of Guillain-Barré syndrome (GBS) is characterized by rapidly progressive and predominantweakness of both upper extremities with hyporeflexia or areflexia. Because the bibracial variantis rare, the pathomechanism and disease course has not been clarified. We report a 42-year-old man withrapidly progressive weakness of both arms. His electrophysiological study showed partial conductionblocks of motor nerves normalized without development of excessive temporal dispersion within 3 weeks. This case suggests that the main pathophysiological mechanism is reversible conduction block and it maybe in the continuous spectrum of axonal motor GBS subtype.
Abstract
The bibrachial variant of Guillain-Barré syndrome (GBS) is characterized by rapidly progressive and predominantweakness of both upper extremities with hyporeflexia or areflexia. Because the bibracial variantis rare, the pathomechanism and disease course has not been clarified. We report a 42-year-old man withrapidly progressive weakness of both arms. His electrophysiological study showed partial conductionblocks of motor nerves normalized without development of excessive temporal dispersion within 3 weeks. This case suggests that the main pathophysiological mechanism is reversible conduction block and it maybe in the continuous spectrum of axonal motor GBS subtype.
참고문헌 (10)
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