양측 원위부 상지를 비대칭적으로 침범한 연소성 근위축증 1예: Hirayama 병
A Case Report of Juvenile Asymmetric Muscular Atrophy of Bilateral Distal Upper Extremity: Hirayama Disease
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초록
We report a 17-year-old man, who had been showing progressive weakness in right forearm and hand for the last 6 months. Nerve conduction studies showed no specific abnormal finding on motor and sensory nerve of both upper and lower extremities. Electromyography of both upper limbs showed significant evidences of denervation in the both flexor carpi radialis, extensor carpi radialis, triceps brachii, extensor indicis proprius, abductor pollicis brevis, and first dorsal interossei. Both brachioradialis and biceps brachii muscles were not affected. Cervical magnetic resonance imaging (MRI) revealed atrophy of the lower cervical cord in a neutral position of neck and a forward displacement of the dural sac with an expanded venous plexus in a flexed position. We present a Korean case of juvenile muscular atrophy suggesting Hirayama disease with its typical clinical, electrophysiological and neuroradiological findings.
Abstract
We report a 17-year-old man, who had been showing progressive weakness in right forearm and hand for the last 6 months. Nerve conduction studies showed no specific abnormal finding on motor and sensory nerve of both upper and lower extremities. Electromyography of both upper limbs showed significant evidences of denervation in the both flexor carpi radialis, extensor carpi radialis, triceps brachii, extensor indicis proprius, abductor pollicis brevis, and first dorsal interossei. Both brachioradialis and biceps brachii muscles were not affected. Cervical magnetic resonance imaging (MRI) revealed atrophy of the lower cervical cord in a neutral position of neck and a forward displacement of the dural sac with an expanded venous plexus in a flexed position. We present a Korean case of juvenile muscular atrophy suggesting Hirayama disease with its typical clinical, electrophysiological and neuroradiological findings.
참고문헌 (12)
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