뒤시엔느 근디스트로피 환자의 영양 상태 평가
Nutritional Status of Duchenne Muscular Dystrophy in South Korea
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Objectives: To investigate nutritional status and various related factors of Korean Duchenne muscular dystrophy(DMD) patients by assessing body mass index(BMI)Methods: Demographical data including height, weight, BMI and nutritional related factors reviewed retrospectively on the medical records of 106 DMD patients. And we also reviewed their functional aspect such as walking ability. We divide the patients into two groups: patients under and more than 19 years old. We divide again each group into four groups along with BMI score: low weight, normal, overweight, and obesity. And then each groups are compared with nutritional related factors and walking ability. Results: The older subjects showed the lower BMI, with statistically significant difference in age among each groups. As a biochemical aspect, In low weight group total lymphocyte count, white blood cell count decreased with statistically significance in patients under 19 years old. As a functional aspect, the subjects in low weight group show the more dependency on ambulation. Conclusions: The accurate evaluation for nutritional status and the continuous nutritional support is required for the rehabilitation of DMD patients.
Abstract
Objectives: To investigate nutritional status and various related factors of Korean Duchenne muscular dystrophy(DMD) patients by assessing body mass index(BMI)Methods: Demographical data including height, weight, BMI and nutritional related factors reviewed retrospectively on the medical records of 106 DMD patients. And we also reviewed their functional aspect such as walking ability. We divide the patients into two groups: patients under and more than 19 years old. We divide again each group into four groups along with BMI score: low weight, normal, overweight, and obesity. And then each groups are compared with nutritional related factors and walking ability. Results: The older subjects showed the lower BMI, with statistically significant difference in age among each groups. As a biochemical aspect, In low weight group total lymphocyte count, white blood cell count decreased with statistically significance in patients under 19 years old. As a functional aspect, the subjects in low weight group show the more dependency on ambulation. Conclusions: The accurate evaluation for nutritional status and the continuous nutritional support is required for the rehabilitation of DMD patients.
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