호산구근막염: 증례보고와 문헌고찰
Eosinophilic fasciitis: A case report with a brief literature review
2
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Eosinophilic fasciitis (EF) is a scleroderma-like immune-allergic disorder of unknown etiology and pathogenesis. This rare disease is characterized by the progressive induration of the skin and soft tissue, and peripheral eosinophilia. Here, we report a case of EF. A 21-year-old female was referred due to edema in the upper and lower extremities for 1 month. Laboratory results were unremarkable except for severe eosinophilia. Parasite infestation, venous thrombosis, and cardiac and renal problems were excluded. Magnetic resonance imaging of both the lower extremities revealed symmetrical thickening and contrast enhancement of crural fascia with adjacent subcutaneous fat infiltration. A full-thickness biopsy at the lower extremity showed infiltration of the fascia by eosinophils, plasma cells, and lymphocytes with marked edema. Thus, this patient was confirmed to have EF and she was treated with systemic corticosteroids, resulting in a remarkable improvement in both edema and eosinophilia.
Abstract
Eosinophilic fasciitis (EF) is a scleroderma-like immune-allergic disorder of unknown etiology and pathogenesis. This rare disease is characterized by the progressive induration of the skin and soft tissue, and peripheral eosinophilia. Here, we report a case of EF. A 21-year-old female was referred due to edema in the upper and lower extremities for 1 month. Laboratory results were unremarkable except for severe eosinophilia. Parasite infestation, venous thrombosis, and cardiac and renal problems were excluded. Magnetic resonance imaging of both the lower extremities revealed symmetrical thickening and contrast enhancement of crural fascia with adjacent subcutaneous fat infiltration. A full-thickness biopsy at the lower extremity showed infiltration of the fascia by eosinophils, plasma cells, and lymphocytes with marked edema. Thus, this patient was confirmed to have EF and she was treated with systemic corticosteroids, resulting in a remarkable improvement in both edema and eosinophilia.
참고문헌 (20)
- Pinal-Fernandez I, "Diagnosis and classification of eosinophilic fasciitis", Autoimmun Rev, 13, pp.379~382 (2014)
- Lakhanpal S, "Eosinophilic fasciitis : clinical spectrum and therapeutic response in 52 cases", Semin Arthritis Rheum, 17, pp.221~231 (1988)
- French LE, "Eosinophilic fasciitis and eosinophilic cellulitis in a patient with abnormal circulating clonal T cells : increased production of interleukin 5 and inhibition by interferon alfa", J Am Acad Dermatol, 49, pp.1170~1174 (2003)
- Fett N, "Eosinophilic fasciitis : current concepts", Clin Dermatol, 36, pp.487~497 (2018)
- Barnes L, "Eosinophilic fasciitis. A pathologic study of twenty cases", Am J Pathol, 96, pp.493~518 (1979)
- Berianu F, "Eosinophilic fasciitis : clinical characteristics and response to methotrexate", Int J Rheum Dis, 18, pp.91~98 (2015)
- 이재욱, "A Case of Eosinophilic Fasciitis: Imaging Findings from Early Diagnosis to Complete Remission", 대한영상의학회지, 71(3), pp.150~154 (2014), 대한영상의학회[DOI]
- 이희선, "A Case of Eosinophilic Fasciitis Presenting as Pitting Edema of the Lower Extremities", Allergy, Asthma & Immunology Research, 6(2), pp.179~182 (2014), 대한천식알레르기학회
- 이상수, "Adalimumab으로 치료된 스테로이드 및 메소트렉세이트 저항성 호산구성 근막염 1예", 대한류마티스학회지, 18(4), pp.306~310 (2011), 대한류마티스학회
- 유인설, "동종 조혈모세포 이식 후 발생한 호산구 근막염(Eosinophilic Fasciitis)", 대한류마티스학회지, 18(1), pp.64~67 (2011), 대한류마티스학회
- Ji Hoon Chun, "Two Cases of Eosinophilic Fasciitis", Annals of Dermatology, 23(1), pp.81~84 (2011), 대한피부과학회
- 구기환, "Peripheral T Cell Lymphoma에 선행하여 발생한 호산구성 근막염 유사 반응", 천식 및 알레르기, 30(3), pp.233~236 (2010), 대한천식알레르기학회
- 정호중, "좌측 하지에 국한된 호산구성 근막염-증례보고-", Annals of Rehabilitation Medicine, 31(4), pp.478~481 (2007), 대한재활의학회
- 황유정, "호산구성 근막염 2예: 초음파의 진단적 유용성과Methotrexate의 치료효과", 대한류마티스학회지, 13(1), pp.56~63 (2006), 대한류마티스학회
- Jin Wuk Hur, "Eosinophilic Fasciitis Associated with Autoimmune Thyroiditis", The Korean Journal of Internal Medicine, 20(2), pp.180~182 (2005), 대한내과학회
- Kim H, "Eosinophilic fasciitis preceding relapse of peripheral T-cell lymphoma", J Korean Med Sci, 15, pp.346~350 (2000)
- Park MK, "A case of eosinophilic fasciitis", Korean J Dermatol, 27, pp.729~733 (1989)
- Lee JB, "Eoxinophilic FAsciitis : report of a case", Korean J Dermatol, 18, pp.361~365 (1980)
- Mertens JS, "Long-term outcome of eosinophilic fasciitis : a cross-sectional evaluation of 35 patients", J Am Acad Dermatol, 77, pp.512~517.e5 (2017)
- Endo Y, "Eosinophilic fasciitis : report of two cases and a systematic review of the literature dealing with clinical variables that predict outcome", Clin Rheumatol, 26, pp.1445~1451 (2007)