Recurrent Superior Mesenteric Artery Syndrome Treated Surgically after Scoliosis Correction in a Patient with Duchenne Muscular Dystrophy
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Superior mesenteric artery (SMA) syndrome is a rare cause of duodenal obstruction that may occur after rapid weight loss or anatomical changes. Patients with Duchenne muscular dystrophy (DMD) are particularly vulnerable due to progressive muscle wasting and scoliosis correction. We report a unique case of recurrent SMA syndrome in a patient with end-stage DMD who required prolonged noninvasive ventilation. After initial nutritional interventions, the patient experienced two recurrences within 15 months. Laparoscopic gastrojejunostomy was safely performed after the second recurrence, despite severely compromised respiratory and cardiac function. This case underscores the importance of early recognition and timely surgical consideration in refractory SMA syndrome, even in patients with advanced neuromuscular disease.
Abstract
Superior mesenteric artery (SMA) syndrome is a rare cause of duodenal obstruction that may occur after rapid weight loss or anatomical changes. Patients with Duchenne muscular dystrophy (DMD) are particularly vulnerable due to progressive muscle wasting and scoliosis correction. We report a unique case of recurrent SMA syndrome in a patient with end-stage DMD who required prolonged noninvasive ventilation. After initial nutritional interventions, the patient experienced two recurrences within 15 months. Laparoscopic gastrojejunostomy was safely performed after the second recurrence, despite severely compromised respiratory and cardiac function. This case underscores the importance of early recognition and timely surgical consideration in refractory SMA syndrome, even in patients with advanced neuromuscular disease.