젊은 성인에서 발생한 고환주위 횡문근육종 1예
A case of the paratesticular rhabdomyosarcoma in the young adult
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Abstract
This paratesticular rhabdomyosarcoma is more frequent in children than in adult. Paratesticular rhabdomyosarcoma accounts for approximately 7% of all rhabdomyosarcomas and is the most common soft tissue sarcoma in childhood, with an annual incidence of four to seven cases per million. The rhabdomyosarcoma originated from paratesticular region is considered to have a good prognosis in comparison with othe rhabdomyosarcomas, despite of the high frequency of retroperitoneal lymph node invasion. This superficial site allows rapid diagnosis and consequently often complete resection of the tumor. The multidisciplinary treatment of paratesticular rhabdomyosarcoma has improved control of the disease with a 2-year survival of 80%. Especially, The outcome for patients with localized paratesticular rhabdomyosarcoma is excellent with the use of the new regimen rather than traditional regimen composed of alkylating agent: an alkylating-free and anthracycline-free regimen is adequate treatment for low-risk patients. We report a case of paratesticular rhabdomyosarcoma of embryonal type in a 17-year-old male who presented left scrotal swelling without tenderness. The diagnosis was confirmed by biopsy. After left radical orchiectomy and hemiscrotectomy, he received VA (Vincristine/Actinomycin-D) chemotherapy.
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