베체트병 환자에서 면역억제치료 후 방실전도장애가 호전된 1예
A Case of Recovered Atrioventricular Conduction in Behçet Disease after Immunotherapy
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초록
Atrioventricular conduction disturbance is a rare clinical manifestation of Behçet disease. We describe a case in which a 48-year-old man complaining of dyspnea on exertion presented with complete atrioventricular block with junctional escape rhythm caused by Behçet disease. He also had moderate aortic regurgitation and mitral regurgitation. MRI and PET scan revealed inflammatory changes involving the ventricular septum and the ascending aorta. Recovery of atrioventricular conduction and improvement of valvular regurgitation were achieved with immunotherapy. Timely diagnosis and treatment of cardiac Behçet disease can prevent unnecessary pacemaker implantation.
Abstract
Atrioventricular conduction disturbance is a rare clinical manifestation of Behçet disease. We describe a case in which a 48-year-old man complaining of dyspnea on exertion presented with complete atrioventricular block with junctional escape rhythm caused by Behçet disease. He also had moderate aortic regurgitation and mitral regurgitation. MRI and PET scan revealed inflammatory changes involving the ventricular septum and the ascending aorta. Recovery of atrioventricular conduction and improvement of valvular regurgitation were achieved with immunotherapy. Timely diagnosis and treatment of cardiac Behçet disease can prevent unnecessary pacemaker implantation.
참고문헌 (10)
- Sakane T, "Behcet's disease", N Engl J Med, 341, pp.1284~1291 (1999)
- zen Y, "Cardiovascular involvement in Behcet's disease", Clin Rheumatol, 29, pp.7~12 (2010)
- Eryol NK, "A case of atrioventricular complete block due to Behcet's disease", Jpn Heart J, 43, pp.697~701 (2002)
- Nojiri C, "Conduction disturbance in Behcet's disease: association with ruptured aneurysm of the sinus of valsalva into the left ventricular cavity", Chest, 86, pp.636~638 (1984)
- Sun RL, "Intra-hisian block associated with unusual etiologies", Pacing Clin Electrophysiol, 10, pp.1117~1124 (1987)
- Unger P, "Subaortic obstruction and complete atrioventricular block in Behcet's disease", Eur J Echocardiogr, 7, pp.250~252 (2006)
- Han JK, "Behcet's disease as a frequently unrecognized cause of aortic regurgitation: suggestive and misleading echocardiography findings", J Am Soc Echocardiogr, 22, pp.1269~1274 (2009)
- Lee I, "Cardiac Behcet disease presenting as aortic valvulitis", aortitis or right heart inflammatory mass: a clinicopathologic study of 12 cases, 2008, pp.32, 390~398
- Lee JS, "A case of ruptured aneurysm of the sinus of valsalva into the left ventricle with complete AV block in Behcet's syndrome", Korean Circ J, 30, pp.107~ (2000)
- 유진석, "Rapidly Progressive Cardiac Manifestation of Behçet’s Disease Involving Conduction System and Aortic Valve", Journal of Cardiovascular Ultrasound, 19(4), pp.199~202 (2011), 한국심초음파학회