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위팔근육위축양측마비의 임상적 특성

Clinical Features of Brachial Amyotrophic Diplegia

권지현|이성현|이상수
대한신경과학회 (Korean Neurological Association)|2006.02|대한신경과학회지 (Journal of the Korean Neurological Association)|제24권 제1호|pp. 47-50

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참고문헌

주제분류신경과학

초록

Abstract

Background: The purpose of this study was to describe a pure lower motor neuron disease in adults that is isolated to the upper limbs over time and to emphasize a differential diagnosis from other motor neuron diseases or motor neuropathies. Methods: We reviewed retrospectively five male patients who had a bilateral upper limb weakness without any sensory changes confirmed by clinical and electrophysiological examinations at least 2 years after onset. Results: Initially weakness remained largely confined to the arms. It then progressed slowly during the follow-up periods ranging from about 5 to 7 years since onset. However, weakness and muscle atrophy spared the lower limbs, respiratory and bulbar musculatures. The patients did not develop any bulbar dysfunctions or pyramidal tract signs. They were still able to ambulate at the end of follow-up. Conclusions: Brachial amyotrophic diplegia presenting with severe weakness that is completely confined to the upper limbs over time, without upper motor neuron signs, might be a stable and relatively benign variant of motor neuron disease. It should be differentiated from other motor neuropathies.

참고문헌 (15)

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관련 논문AI추천

상완근위축양측마비의 경과 관찰 2례 - 증례보고 -김경렬, 김우섭, 박영옥, 이승화, 장철호대한근전도전기진단의학회 · 대한근전도 전기진단의학회지2010 · 제12권 제1호Kennedy병의 임상적, 전기 진단적 특징김광국, 오병철, 임영민대한임상신경생리학회 · Annals of Clinical Neurophysiology2003 · 제5권 제1호하지에 생긴 양성 일지성 근위축 2예이동국대한임상신경생리학회 · Annals of Clinical Neurophysiology2000 · 제2권 제2호원위형 척수성 근위축증과 감별된 제III형 근위형 척수성 근위축증 1례-증례 보고-김형섭, 문재호, 박용범, 박윤길, 이상철, 이수현, 조수경대한재활의학회 · Annals of Rehabilitation Medicine2007 · 제31권 제1호근위축성 측삭경화증의 진단에 있어서 전기진단학적 검사이동국대한임상신경생리학회 · Annals of Clinical Neurophysiology2004 · 제6권 제1호감각신경전도 이상을 동반한 근위축성측색경화증김병준, 서상혁, 서연림, 신경진, 안재영, 이택준대한임상신경생리학회 · Annals of Clinical Neurophysiology2005 · 제7권 제2호

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