양안에 발생한 나팔꽃증후군 1예
A Case of Bilateral Morning Glory Syndrome
0
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
목적: 양안에 나팔꽃증후군으로 진단받은 1예가 있어 보고하고자 한다. 증례요약: 2002년 5월 본원에 6세 여환이 좌안의 시력저하를 주소로 내원하였다. 최대교정시력은 조절마비검사상 우안 0.8, 좌안 0.1로 좌안의 시력 저하가 있었고, 세극등현미경검사상 좌안의 백내장이 확인되었으며 안저검사상 양안의 나팔꽃증후군으로 진단하였다. 내원 한 달 후 좌안 수정체 초음파유화술 및 인공수정체삽입술, 홍채유착해리술, 부분 유리체절제술을 시행하였다. 술 후 5년 2개월후 내원 시 최대교정시력은 현성굴절검사상 우안 0.5, 좌안 0.1이었으며, 세극등현미경검사 및 안저검사상 수술 직후와 큰 변화 없었다. 빛간섭단층촬영상 우안의 중심황반두께는 감소되었으며 우안의 생리적 암점 증가와 좌안의 주변부 시야 감소 소견을 보였다. 결론: 나팔꽃증후군은 주로 단안에서 발생한다고 알려져 있으나 본 사례에서는 양안에 발생하였다. 전안부와 망막의 이상이 동반될 수 있으므로 향후 정기적으로 추적 관찰을 하여야 하겠다.
Abstract
Purpose: To report a bilateral case of morning glory syndrome. Case summary: On May 30, 2002, a six-year-old patient visited our clinic with impaired visual acuity of her left eye and was diagnosed as having a cataract on her left eye superimposed on a bilateral morning glory anomaly. According to cycloplegic refraction, the patient’s corrected visions was 0.8 in the right eye and 0.1 in the left. On June 20, 2002, the patient received ultrasonographic phacoemulsification, intraocular lens implantation, synechiolysis and partial vitectomy in her left eye. Approximately 5.2 years after the surgery, according to manifest refraction, the patient’s corrected visions were 0.8 in the right eye and 0.1 in the left, no prominent postoperative changes were observed on slit lamp microscopy and fundus examinations. The thickness of the central macula of her right eye had decreased according to optical coherence tomography; the physiologic scotoma size of the patient’s right eye had increased with narrowed peripheral visual field of her left eye. Conclusions: Although monocular morning glory anomaly has previously been reported to occur, in the present study case, the anomaly occurred bilaterally. In morning glory patients, strabismus examination and additional evaluation of a patient’s general state should be performed along with a regular fundus examination.
참고문헌 (22)
- Kindler P, "Morning glory syndrome : unusual optic disk anomaly", Am J Ophthalmology, 69, pp.376~384 (1970)
- Krause U, "Three cases of the morning glory syndrome", Acta Ophthalmology, 50, pp.188~198 (1972)
- Steinkuller PG, "The morning glory disk anomaly: case report and literature review", J Pediatr Ophthalmol Strabismus, 17, pp.81~87 (1980)
- Bayer WB, "Morning Glory Syndrome: A functional analysis including fluoresein angiography, ultrasonography and computerized tomography", Ophthalmology, 89, pp.1362~1367 (1982)
- Dempster AG, "The morning golry syndrome-a mesodermal defect?", Ophthalmologica, 187, pp.22~23 (1983)
- Goldhammer Y, "Optic nerve anomalies in basal encephalocele", Arch Ophthalmol, 93, pp.115~118 (1975)
- Brodsky MC, "Congenital anomalies of the optic disc. In Walsh & Hoyt’s Clinical Neuro-ophthalmology, 5th ed", pp.775~823 (1998), Williams & Wilkins
- Itaura T, "-", J Neurosurg, 77, pp.949~951 (1992)
- De Laey JJ, "The ‘morning glory’ syndrome", Ophthalmic Pediatr Genet, 5, pp.117~124 (1985)
- Akiyama K, "Retinal detachment in Morning Glory syndrome", Ophthalmic surg, 15, pp.841~843 (1984)
- Miller NR, "Anormalies of the optic disc. In The essentials: Walsh & Hoyl’s Clinical Neurophthalmology. 5th ed", pp.117~123 (1999), Williams & Williams
- Nilanjama D, "Bilateral Morning Glory Disc Anomaly", Indian J Ophthalmol, 51, pp.182~184 (2003)
- Nagy V, "Morning glory syndrome- a clinical study of two cases", Klin Monatsbl Augenheilkd, 219, pp.801~805 (2002)
- Pollock S, "The morning glory disc anomaly: contractile movement, classification and embryogenesis", Doc Ophthalmol, 65, pp.439~460 (1987)
- Loudot C, "Rehabilitation on functional ambylopia in morning glory syndrome", J Fr Ophthalmol, 30, pp.998~1001 (2007)
- Caprioli J, "Basal encephalocele and morning glory syndrome", Br J Ophthalmol, 67, pp.349~351 (1983)
- Apple DJ, "Congenital anomalies of the optic disc", Surv Ophthalmol, 27, pp.3~ (1982)
- Traboulsi EI, "The spectrum in the morphology of the so-called “morning glory disc anomaly”", J Pediatr Ophthalmol Strabismus, 25, pp.93~98 (1988)
- Yoo YS, "A case of morning glory syndrome", J Korean Ophthalmol Soc, 29, pp.749~752 (1988)
- Haik BG, "Retinal detachment in the morning glory anomaly", Ophthamology, 91, pp.1638~1647 (1984)
- Kawano K, "Duane’s retraction syndrome associated with morning glory syndrome", J Pediatr Ophthalmol Strabismus, 18, pp.51~54 (1981)
- Savell J, "Optic nerve colobomas of autosomal dominant hereditary", Arch Ophthalmol, 94, pp.395~400 (1982)