Churg-Strauss syndrome that presented with mediastinal lymphadenopathy and calculous cholecystitis
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Churg-Strauss syndrome (CSS) is a systemic disorder characterized by bronchial asthma, hypereosinophilia, and systemic vasculitis. The American College of Rheumatology (ACR) classification criteria in patients with biopsy-proven vasculitis is the most widely used today. These criteria include asthma, greater than 10% peripheral eosinophilia, mono- or polyneuropathy, migratory pulmonary infiltrates, sinus anomalies, and extravascular eosinophils in the biopsy. The presence of four of these criteria in a patient with biopsy-proven vasculitis has a sensitivity of 85% and a specificity of 99.7% for CSS [1]. Involvement of the lung, skin, gastrointestinal tract, and nervous system are common in CSS, but involvement of the mediastinal lymph node (LN) and gallbladder (GB) containing stones are less common. We, herein, report and discuss a special CSS case involving the mediastinal LN and GB containing stones, as well as lung parenchyme.
Abstract
Churg-Strauss syndrome (CSS) is a systemic disorder characterized by bronchial asthma, hypereosinophilia, and systemic vasculitis. The American College of Rheumatology (ACR) classification criteria in patients with biopsy-proven vasculitis is the most widely used today. These criteria include asthma, greater than 10% peripheral eosinophilia, mono- or polyneuropathy, migratory pulmonary infiltrates, sinus anomalies, and extravascular eosinophils in the biopsy. The presence of four of these criteria in a patient with biopsy-proven vasculitis has a sensitivity of 85% and a specificity of 99.7% for CSS [1]. Involvement of the lung, skin, gastrointestinal tract, and nervous system are common in CSS, but involvement of the mediastinal lymph node (LN) and gallbladder (GB) containing stones are less common. We, herein, report and discuss a special CSS case involving the mediastinal LN and GB containing stones, as well as lung parenchyme.
참고문헌 (5)
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