Incidentally Detected Situs Ambiguous in Adults
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초록
Situs ambiguous is rare congenital anomaly in adults. In 2 adult patients who admitted for different cardiac problems, situs ambiguous with polysplenia was detected. A 42-year-old male admitted for radio frequent catheter ablation of atrial fibrillation, and he had left-sided inferior vena cava (IVC), hepatic segment of IVC interruption with hemiazygos continuation, multiple spleens and intestinal malrotation. And in a 52-year-old female case who was hospitalized due to infective endocarditis after implanting pacemaker for sick sinus syndrome, multiple spleens, left-sided stomach, bilateral liver with midline gallbladder, and left-sided IVC were found. Those findings were consistent with situs ambiguous with polysplenia, but their features were distinctive.
Abstract
Situs ambiguous is rare congenital anomaly in adults. In 2 adult patients who admitted for different cardiac problems, situs ambiguous with polysplenia was detected. A 42-year-old male admitted for radio frequent catheter ablation of atrial fibrillation, and he had left-sided inferior vena cava (IVC), hepatic segment of IVC interruption with hemiazygos continuation, multiple spleens and intestinal malrotation. And in a 52-year-old female case who was hospitalized due to infective endocarditis after implanting pacemaker for sick sinus syndrome, multiple spleens, left-sided stomach, bilateral liver with midline gallbladder, and left-sided IVC were found. Those findings were consistent with situs ambiguous with polysplenia, but their features were distinctive.
참고문헌 (16)
- Fulcher AS, "Abdominal manifestations of situs anomalies in adults", Radiographics, 22, pp.1439~1456 (2002)
- Jacobs JP, "The nomenclature, definition and classification of cardiac structures in the setting of heterotaxy", Cardiol Young, 17(2), pp.1~28 (2007)
- Brandenburg VM, "Heterotaxy syndrome with severe pulmonary hypertension in an adult", South Med J, 95, pp.536~538 (2002)
- Rose V, "Syndromes of asplenia and polysplenia. A review of cardiac and non-cardiac malformations in 60 cases withspecial reference to diagnosis and prognosis", Br Heart J, 37, pp.840~852 (1975)
- Gatrad AR, "Consanguinity and complex cardiac anomalies with situs ambiguus", Arch Dis Child, 59, pp.242~245 (1984)
- Peoples WM, "Polysplenia: a review of 146 cases", Pediatr Cardiol, 4, pp.129~137 (1983)
- Pepes S, "Prenatal diagnosis of left atrial isomerism", Heart, 95, pp.1974~1977 (2009)
- 조윤형, "A Case of Noncompaction of the Ventricular Myocardium Combined with Situs Ambiguous with Polysplenia", Yonsei Medical Journal, 48(6), pp.1052~1055 (2007), 연세대학교의과대학
- 손관협, "하대정맥 중절과 다비장증을 동반한 좌이성체에서 대동맥축착 1예", Journal of Cardiovascular Ultrasound, 15(1), pp.27~29 (2007), 한국심초음파학회
- Jae Hun Kim, "Heterotaxia Syndrome with Intraluminal Duodenal Diverticulum", 대한외과학회지, 79(1), pp.75~78 (2010), 대한외과학회
- Cheon IS, "Hemiazygos continuation of left inferior vena cava draining into the right atrium via persistent left superior vena cava: a variant of polysplenia syndrome mimicking aortic dissection", Korean Circ J, 28, pp.440~447 (1998)
- 박용범, "중장의 비회전과 십이지장 전치 간문맥을 포함한 다발성 복강내 기형 1예", 대한내과학회지, 73(5), pp.548~551 (2007), 대한내과학회
- Applegate KE, "Situs revisited: imaging of the heterotaxy syndrome", Radiographics, 19, pp.837~852 (1999)
- Bartram U, "Congenitally interrupted inferior vena cava without other features of the heterotaxy syndrome: report of five cases and characterization of a rare entity", Pediatr Dev Pathol, 11, pp.266~273 (2008)
- Miranda R, "Superior approach for radiofrequency ablation of atrio-ventricular nodal reentrant tachycardia in a patient with anomalous inferior vena cava and azygos continuation", Europace, 12, pp.908~909 (2010)
- Lee S, "Persistent left superior caval vein with absent right superior caval vein: importance of awareness", Cardiol Young, pp.1~3 (2011)