Right Atrial Paraganglioma: An Extremely Rare Primary Cardiac Neoplasm Mimicking Myxoma
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In this report, we present a case of 35-year-old lady who had presented with atypical chest pain and exertional breathlessness forpast six months. Transthoracic and transesophageal echocardiograms showed a well-circumscribed, echo-dense mass in the rightatrium, attached to the interatrial septum at the level of atrioventricular junction and in the vicinity of coronary sinus ostium. Sheunderwent successful resection of the cardiac mass. Histopathology revealed paraganglioma, which was reconfirmed by immunohistochemistrystudy. This represents an extremely rare presentation as primary cardiac tumors are 20-times less common thanmetastatic tumors and paraganglioma is one of the rarest primary cardiac tumors, accounting for < 1% of all cases.
Abstract
In this report, we present a case of 35-year-old lady who had presented with atypical chest pain and exertional breathlessness forpast six months. Transthoracic and transesophageal echocardiograms showed a well-circumscribed, echo-dense mass in the rightatrium, attached to the interatrial septum at the level of atrioventricular junction and in the vicinity of coronary sinus ostium. Sheunderwent successful resection of the cardiac mass. Histopathology revealed paraganglioma, which was reconfirmed by immunohistochemistrystudy. This represents an extremely rare presentation as primary cardiac tumors are 20-times less common thanmetastatic tumors and paraganglioma is one of the rarest primary cardiac tumors, accounting for < 1% of all cases.
참고문헌 (10)
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