심장의 벽운동 이상과 심낭삼출로 발현된 과호산구 증가 증후군 1예
A case of idiopathic hypereosinophilic syndrome manifested as regional wall motion abnormalities in echocardiogram and pericardial effusion
1
조회
0
다운로드
1
인용
0
참고문헌
키워드
초록
Idiopathic hypereosinophilic syndrome is characterized by unexplained blood eosinophilia > 1500/mm3 for more than 6 months and eosinophilic infiltration of several organs. A major source of the morbidity and mortality of this syndrome is the associated cardiac involvement. The typical cardiac involvement includes endocardial fibrosis and mural thrombus. We report a case of idiopathic hypereosinophilic syndrome manifested as multiple regional wall motion abnormalities and moderate pericardial effusion on transthoracic echocardiography that was successfully treated by pericardiostomy and steroid therapy. (Korean J Med 75:484-487, 2008)
Abstract
Idiopathic hypereosinophilic syndrome is characterized by unexplained blood eosinophilia > 1500/mm3 for more than 6 months and eosinophilic infiltration of several organs. A major source of the morbidity and mortality of this syndrome is the associated cardiac involvement. The typical cardiac involvement includes endocardial fibrosis and mural thrombus. We report a case of idiopathic hypereosinophilic syndrome manifested as multiple regional wall motion abnormalities and moderate pericardial effusion on transthoracic echocardiography that was successfully treated by pericardiostomy and steroid therapy. (Korean J Med 75:484-487, 2008)
참고문헌 (14)
- Weller PF, "The idiopathic hypereosinophilic syndrome", Blood, 83, pp.2759~2779 (1994)
- Chusid MJ, "The hypereosinophilic syndrome: analysis of fourteen cases with review of literature", Medicine, 54, pp.1~27 (1975)
- Fauci AS, "The idiopathic hypereosinophilic syndrome: clinical, pathophysiologic, and therapeutic considerations", Ann Intern Med, 97, pp.78~92 (1982)
- Hardy WR, "The hypereosinophilic syndromes", Ann Intern Med, 68, pp.1220~1229 (1968)
- Makino S, "Eosinophils: biological and clinical aspects", pp.403~ (1992), CRC press
- Desreumaux P, "Synthesis of interleukin-5 by activated eosinophils in patients with eosinophilic heart diseases", Blood, 82, pp.1553~1560 (1993)
- Brockington IF, "Eosinophilia and endomyocardial fibrosis", Postgrad Med J, 48, pp.740~741 (1972)
- Wang JG, "The principal eosinophil peroxidase product, HOSCN, is a uniquely potent phagocyte oxidant inducer of endothelial cell tissue factor activity: a potential mechanism for thrombosis in eosinophilic inflammatory states", Blood, 107, pp.558~565 (2006)
- Ommen SR, "Clinical and echocardiographic features of hypereosinophilic syndromes", Am J Cardiol, 86, pp.110~113 (2000)
- 박용호, "급성 호산구성 심근염으로 나타난 과호산구 증후군 1예", 대한내과학회지, 66(3), pp.284~287 (2004), 대한내과학회
- Parrillo JE, "Therapy of the hypereosinophilic syndrome", Ann Intern Med, 89, pp.167~172 (1978)
- Moore PM, "Neurologic dysfuction in the idiopathic hypereosinophilic syndrome", Ann Intern Med, 102, pp.109~114 (1985)
- Klion AD, "Elevated serum tryptase levels identify a subset of patients with a myeloproliferative variant of idiopathic hypereosinophilic syndrome associated with tissue fibrosis, poor prognosis, and imatinib responsiveness", Blood, 101, pp.4660~4666 (2003)
- Parrillo JE, "Immunologic reactivity in the hypereosinophilic syndrome", J Allergy Clin Immunol, 64, pp.113~121 (1979)
