원발성 자가면역 골수섬유증 1예
A Case of Primary Autoimmune Myelofibrosis
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초록
Primary autoimmune myelofibrosis, the development of which is not preceded by a well-defined autoimmune disease, has recentlybeen defined as a distinct clinicopathologic syndrome. We report herein a case of a 68-year-old woman who was diagnosedwith primary autoimmune myelofibrosis and present a review of the literature. The patient manifested peripheral pancytopenia, waspositive for autoantibodies, and developed myelofibrosis with no preceding autoimmune or hematologic disorders. Her conditionwas dramatically improved after administration of prednisolone.
Abstract
Primary autoimmune myelofibrosis, the development of which is not preceded by a well-defined autoimmune disease, has recentlybeen defined as a distinct clinicopathologic syndrome. We report herein a case of a 68-year-old woman who was diagnosedwith primary autoimmune myelofibrosis and present a review of the literature. The patient manifested peripheral pancytopenia, waspositive for autoantibodies, and developed myelofibrosis with no preceding autoimmune or hematologic disorders. Her conditionwas dramatically improved after administration of prednisolone.
참고문헌 (11)
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