미만성 폐포출혈증후군으로 발생한 척-스트라우스 증후군의 1예
Churg-Strauss Syndrome Presenting with Diffuse Alveolar Hemorrhage
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척-스트라우스 증후군은 스테로이드 및 면역억제 치료로적절하게 치료하지 않을 경우 예후가 좋지 않고 임상적 관해에 도달하기 어려운 질환이다. 본 증례 환자의 경우 항호중구성 항체 음성 혈관염의 척-스트라우스 증후군으로 스테로이드 및 cyclophosphamide 치료를 시행하였고 임상증상이호전된 증례이다. 따라서 척-스트라우스 증후군이라는 질병을 잘 이해하고 진단하여 치료하는 것은 환자의 예후 및 경과에 중요한 역할을 한다.
Abstract
Churg-Strauss syndrome (CSS), known as eosinophilic granulomatosis with polyangiitis, is a rare type of systemic vasculitis characterized by the presence of asthma, peripheral eosinophilia, and necrotizing vasculitis with eosinophilic infiltration of multiple organs. Approximately 3-4% of all CSS cases are associated with alveolar hemorrhage. Untreated CSS may lead to a poor prognosis, but glucocorticoid and cytotoxic agent treatments may result in clinical remission. The careful diagnosis and understanding of CSS is important for making treatment decisions and providing effective care. Here, we report a case of CSS with diffuse alveolar hemorrhage.
참고문헌 (10)
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