심한 우심실 유출로 폐쇄가 동반된 양심실 비후성 심근증 1예
Biventricular Hypertrophic Cardiomyopathy with Severe Right Ventricular Outflow Track Obstruction
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초록
Hypertrophic cardiomyopathy (HCM) has diverse pathophysiological and clinical features, according to the extent and severity of the hypertrophy development. Hypertrophy mostly involves the left ventricle and sometimes causes a left ventricular outflow tract obstruction. Right ventricular involvement is less frequent, and even the severe form of a right ventricular outflow tract (RVOT) obstruction by concurrent right ventricular hypertrophy in a patient with HCM is rare. We report a case of biventricular HCM with a clinically, morphologically, and hemodynamically significant RVOT obstruction, which had been treated successfully with surgical myectomy.
Abstract
Hypertrophic cardiomyopathy (HCM) has diverse pathophysiological and clinical features, according to the extent and severity of the hypertrophy development. Hypertrophy mostly involves the left ventricle and sometimes causes a left ventricular outflow tract obstruction. Right ventricular involvement is less frequent, and even the severe form of a right ventricular outflow tract (RVOT) obstruction by concurrent right ventricular hypertrophy in a patient with HCM is rare. We report a case of biventricular HCM with a clinically, morphologically, and hemodynamically significant RVOT obstruction, which had been treated successfully with surgical myectomy.
참고문헌 (5)
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- Borisov KV, "Surgical correction of hypertrophic obstructive cardiomyopathy in patients with simultaneous obstruction of left ventricular midcavity and right ventricular outflow tract", Eur J Cardiothorac Surg, 43, pp.67~72 (2013)
- Quintana E, "Surgery for biventricular obstruction in hypertrophic cardiomyopathy in children and young adults : technique and outcomes", Eur J Cardiothorac Surg, 47, pp.1006~1012 (2015)