A CASE OF CONGENITAL HIGH AIRWAY OBSTRUCTION SYNDROME CAUSED BY COMPLETE TRACHEAL OBSTRUCTION WITH ASSOCIATED ANOMALIES
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초록
Congenital high airway obstruction syndrome (CHAOS) is caused when the upper airway is obstructed or severely narrowed. The prenatal ultrasound fi ndings of CHAOS include large echogenic lungs, inverted diaphragms, dilated airways, and fetal ascites and/or hydrops. Recently, exutero intrapartum treatment (EXIT) procedure or fetoscopic tracheostomy are being widely used for the treatment of CHAOS. However, CHAOS with early presentation of hydrops confers ominous sign even with EXIT procedure. We report a case of CHAOS with hydrops and associated anomalies that was confi rmed by autopsy.
Abstract
Congenital high airway obstruction syndrome (CHAOS) is caused when the upper airway is obstructed or severely narrowed. The prenatal ultrasound fi ndings of CHAOS include large echogenic lungs, inverted diaphragms, dilated airways, and fetal ascites and/or hydrops. Recently, exutero intrapartum treatment (EXIT) procedure or fetoscopic tracheostomy are being widely used for the treatment of CHAOS. However, CHAOS with early presentation of hydrops confers ominous sign even with EXIT procedure. We report a case of CHAOS with hydrops and associated anomalies that was confi rmed by autopsy.
참고문헌 (10)
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