출생 직후 진단된 Herlyn-Werner-Wunderlich syndrome 1예
A case of Herlyn-Werner-Wunderlich syndrome diagnosed in asymptomatic newborn
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초록
Herlyn-Werner-Wunderlich (HWW) syndrome은 중복자궁, 한쪽 질의 맹관, 동측 신장의 무발생을 특징으로 한다. 대부분 초경이 시작된직후인 12-13세 때 증상이 발현되어 진단되며, 주로 골반 자기공명영상을 통해 진단된다. 질맹관조대술이나 제거술로 쉽게 치료 가능하며, 치료하지 않을 경우 불임, 자궁내막증, 복강내유착, 난관농양, 자궁농양, 습관성 유산 등의 여러 합병증이 발생한다. 저자들은 산전초음파에서 비뇨기계 이상이 의심되었던 태아에서, 출생 직후 특이 증상이 없었으나 진단된 HWW syndrome 1예를 경험하였기에 간단한 문헌고찰과 함께 보고하는 바이다.
Abstract
Herlyn-Werner-Wunderlich (HWW) syndrome is characterized by the triad of uterine didelphys, obstructed hemivagina, ipsilateral renal agenesis. Symptoms generally occur just after menarche about 12 to 13 years old and it is usually diagnosed by pelvis magnetic resonance imaging. It can be treated by marsupialization of obstructed hemivagina or vaginal septum resection. It can be complicated by infertility, endometriosis, pelvic cavity adhesion, pyosalpinx, pyocolpos, and recurrent miscarriage. Together with a brief review of literature, we report a case of HWW syndrome diagnosed in asymptomatic newborn who was suspected to have a genitourinary anomaly on prenatal ultrasonography.
참고문헌 (14)
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