경도인지장애와 운동과다증을 동반한 Fahr 환자 1예
A Case of Fahr Disease with Mild Cognitive Impairment and Hyperkinesia
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초록
A 66-yr-old woman presented with progressive cognitive decline and mild hyperkinetic motor symptoms. Neuropsychological evaluation revealed impairment of memory and frontal executive functions with normal activities of daily living, indicating a mild cognitive impairment. Brain imaging showed extensive calcification involving bilateral basal ganglia, thalamus, occipital cortex and cerebellum consistent with Fahr disease. FDG-PET showed diffuse glucose hypometabolism in bilateral fronto-temporo-parietal cortices, suggesting the disruption of frontal subcortical circuit to be probably associated with the cognitive impairment of the patient.
Abstract
A 66-yr-old woman presented with progressive cognitive decline and mild hyperkinetic motor symptoms. Neuropsychological evaluation revealed impairment of memory and frontal executive functions with normal activities of daily living, indicating a mild cognitive impairment. Brain imaging showed extensive calcification involving bilateral basal ganglia, thalamus, occipital cortex and cerebellum consistent with Fahr disease. FDG-PET showed diffuse glucose hypometabolism in bilateral fronto-temporo-parietal cortices, suggesting the disruption of frontal subcortical circuit to be probably associated with the cognitive impairment of the patient.
참고문헌 (19)
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