Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion
0
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Pierre Robin sequence (PRS), also called Robin sequence, is a congenital anomaly characterized by a triad of micrognathia, glossoptosis, and upper airway obstruction. Infants with PRS can present with varying degrees of respiratory difficulty secondary to upper airway obstruction. There has been no consensus for the treatment of upper airway obstruction in infants with PRS, but recent studies recommend attempting non-surgical interventions before surgical treatment. In this case report, we present 3 cases of infants diagnosed with PRS who showed persistent respiratory difficulties after birth. Before considering surgical intervention, insertion of a nasopharyngeal airway was attempted in these infants. Following this procedure, symptoms of upper airway obstruction were relieved, and all infants were discharged without surgical interventions; the nasopharyngeal airway was removed 1 to 2 months later. To date, no infant has shown signs of upper airway obstruction. Nasopharyngeal airway insertion is a highly effective and less invasive treatment option for infants with PRS. However, it is not widely known and used in Korea. Nasopharyngeal airway insertion can be preferentially considered before surgical intervention for upper airway obstruction in such infants.
Abstract
Pierre Robin sequence (PRS), also called Robin sequence, is a congenital anomaly characterized by a triad of micrognathia, glossoptosis, and upper airway obstruction. Infants with PRS can present with varying degrees of respiratory difficulty secondary to upper airway obstruction. There has been no consensus for the treatment of upper airway obstruction in infants with PRS, but recent studies recommend attempting non-surgical interventions before surgical treatment. In this case report, we present 3 cases of infants diagnosed with PRS who showed persistent respiratory difficulties after birth. Before considering surgical intervention, insertion of a nasopharyngeal airway was attempted in these infants. Following this procedure, symptoms of upper airway obstruction were relieved, and all infants were discharged without surgical interventions; the nasopharyngeal airway was removed 1 to 2 months later. To date, no infant has shown signs of upper airway obstruction. Nasopharyngeal airway insertion is a highly effective and less invasive treatment option for infants with PRS. However, it is not widely known and used in Korea. Nasopharyngeal airway insertion can be preferentially considered before surgical intervention for upper airway obstruction in such infants.
참고문헌 (15)
- Cote A, "Pierre Robin sequence:review of diagnostic and treatment challenges", Int J Pediatr Otorhinolaryngol, 79, pp.451~464 (2015)
- Rathe M, "Pierre Robin sequence: management of respiratory and feeding complications during the first year of life in a tertiary referral centre", Int J Pediatr Otorhinolaryngol, 79, pp.1206~1212 (2015)
- van Lieshout MJ, "Non-surgical and surgical interventions for airway obstruction in children with Robin sequence", J Craniomaxillofac Surg, 44, pp.1871~1879 (2016)
- Cladis F, "Pierre Robin sequence: a perioperative review", Anesth Analg, 119, pp.400~412 (2014)
- Gomez OJ, "Pierre Robin sequence:an evidence-based treatment proposal", J Craniofac Surg, 29, pp.332~338 (2018)
- Robin P., "La chute de la base de la langue considérée comme une nouvelle cause de gêne dans la respiration naso-pharyngienne", Bull Acad Med, 89, pp.37~41 (1923)
- Li WY, "Airway management in Pierre Robin sequence:the Vancouver classification", Plast Surg (Oakv), 25, pp.14~20 (2017)
- Chang IK, "Pierre Robin syndrome: case report", J Korean Surg Soc, 11, pp.413~418 (1969)
- 이장원, "피에르 로빈 연속증의 치료로써 치조 보호 장치를 이용한 혀-하순 유착술", Archives of Plastic Surgery, 38(4), pp.547~551 (2011), 대한성형외과학회
- 유선열, "Pierre Robin sequence 환아에서 하악골신장술", 대한구강악안면외과학회지, 34(4), pp.460~467 (2008), 대한구강악안면외과학회
- Roberts K, "The nasopharyngeal airway:dispelling myths and establishing the facts", Emerg Med J, 22, pp.394~396 (2005)
- Tweedie DJ, "The nasopharyngeal prong airway: an effective post-operative adjunct after adenotonsillectomy for obstructive sleep apnoea in children", Int J Pediatr Otorhinolaryngol, 71, pp.563~569 (2007)
- Abel F, "The successful use of the nasopharyngeal airway in Pierre Robin sequence: an 11-year experience", Arch Dis Child, 97, pp.331~334 (2012)
- Drago Marquezini Salmen IC, "In situ and home care nasopharyngeal intubation improves respiratory condition and prevents surgical procedures in early infancy of severe cases of robin sequence", Biomed Res Int, 2015, pp.608905~ (2015)
- Evans KN, "Robin sequence: from diagnosis to development of an effective management plan", Pediatrics, 127, pp.936~948 (2011)