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간문맥혈전증을 동반한 특발성 문맥고혈압 환자에서 Protein C, Protein S 결핍 1예

Deficiencies in proteins C and S in a patient with idiopathic portal hypertension accompanied by portal vein thrombosis

한광협|전재윤|김도영|전영은|이현정|김민주|박영년|박준용|안상훈|황세나
대한간학회 (The korean Association for the Study of the Liver)|2010.06|Clinical and Molecular Hepatology|제16권 제2호|pp. 176-181

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참고문헌

키워드

Protein CProtein S문맥압항진증혈전증Portal hypertension; Thrombosis; Protein C deficiency; Protein S deficiency

초록

간문맥의 혈전 소견을 동반한 특발성 문맥압항진증 환자에서 자가면역질환, 종양 등 다른 원인이 없이 protein C, protein S의 결핍을 보인 사례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Abstract

Portal vein thrombosis (PVT) is an uncommon cause of presinusoidal portal hypertension. Among various hepatoportal disorders, noncirrhotic portal hypertension conditions such as idiopathic portal hypertension (IPH) are considered to have a close relation with PVT. PVT is known to have several predisposing conditions, including infection, malignancies, and coagulation disorders. There is growing interest and recognition that deficiencies in proteins C and S are associated with a hypercoagulable state. These deficiencies are regarded as key factors of systemic hypercoagulability and recurrent venous thromboembolism. We report the case of a 19-year-old male diagnosed as IPH with PVT and combined deficiencies in proteins C and S.

참고문헌 (19)

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관련 논문AI추천

간문맥 혈전증: 역학, 진단 및 치료에 관하여김세화, 박상종, 서준영, 유양재, 이아영대한내과학회 · 대한내과학회지2023 · 제98권 제4호단백질 C와 S 결핍증 환자에서 발생한 자발성 신동맥 박리 1예서재현, 유현아, 이관현, 이래석, 임예지, 장경윤, 황대연대한내과학회 · 대한내과학회지2013 · 제84권 제1호폐농양과 동반된 간문맥 혈전증 1예김영묵, 박성남, 임주견대한내과학회 · 대한내과학회지2012 · 제82권 제1호특발성 문맥압 항진증 8예의 임상 및 병리학적 분석김경모, 김경은, 유은실, 임영석대한병리학회 · Journal of Pathology and Translational Medicine2006 · 제40권 제5호Endovascular intervention for portal vein system thrombosis in a patient with protein S deficiency: A case reportIl Han Song, Min Jeong Choi소화기인터벤션의학회 · International Journal of Gastrointestinal Intervention2025 · 제14권 제2호Antithrombin Ⅲ, Protein C and Protein S 결핍 여성에서 경구 피임약 복용 중에 발생한 정맥혈전증 1예김주선, 김진학, 배성준, 윤연정, 이신애대한산부인과학회 · Obstetrics & Gynecology Science2006 · 제49권 제6호

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