MRI Findings of Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA syndrome) with a Blind Megaureter: Case Report
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Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is anuncommon congenital abnormality of the female urogenital tract characterized bythe triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. A 13-year-old female presented with acute lower abdominal pain. Magneticresonance imaging (MRI) revealed uterine didelphys, hematometrocolpos, obstructedhemivagina, and right ipsilateral agenesis, consistent with OHVIRA syndrome. Also, awell-defined mass with fluid signal intensity, mimicking adnexal neoplasm was seenin the right lower pelvic cavity adjacent to the posterior wall of the bladder. Vaginalseptotomy and drainage of hematometrocolpos were done initially, but unilateralhysterectomy was later performed to relieve the patient’s symptoms. The cystic massin the right lower pelvic cavity was also excised and confirmed as a blind megaureter.
Abstract
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is anuncommon congenital abnormality of the female urogenital tract characterized bythe triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. A 13-year-old female presented with acute lower abdominal pain. Magneticresonance imaging (MRI) revealed uterine didelphys, hematometrocolpos, obstructedhemivagina, and right ipsilateral agenesis, consistent with OHVIRA syndrome. Also, awell-defined mass with fluid signal intensity, mimicking adnexal neoplasm was seenin the right lower pelvic cavity adjacent to the posterior wall of the bladder. Vaginalseptotomy and drainage of hematometrocolpos were done initially, but unilateralhysterectomy was later performed to relieve the patient’s symptoms. The cystic massin the right lower pelvic cavity was also excised and confirmed as a blind megaureter.
참고문헌 (9)
- Lopes Dias J, "Herlyn-Werner-Wunderlich syndrome: pre- and post-surgical MRI and US findings", Abdom Imaging (2015)
- Orazi C, "Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases", Pediatr Radiol, 37, pp.657~665 (2007)
- Del Vescovo R, "Herlyn-Werner- Wunderlich syndrome: MRI findings, radiological guide (two cases and literature review), and differential diagnosis", BMC Med Imaging, 12, pp.4~ (2012)
- Behr SC, "Imaging of mullerian duct anomalies", Radiographics, 32, pp.E233~E250 (2012)
- Smith NA, "Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: management and follow-up", Fertil Steril, 87, pp.918~922 (2007)
- Dobrocký I, "Ectopic blind ureter with ipsilateral renal agenesis: a case report", Eur J Radiol, 20, pp.77~79 (1995)
- La Fianza A, "Blind megaureter with ipsilateral renal agenesis and mullerian anomaly: MR findings in a case", Clin Imaging, 23, pp.184~186 (1999)
- Han B, "Uterine didelphys associated with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome", Radiology Case Reports, 5, pp.327~ (2010)
- Donnez O, "Didelphic uterus and obstructed hemivagina: recurrent hematometra in spite of appropriate classic surgical treatment", Gynecol Obstet Invest, 63, pp.98~101 (2007)