CT and MRI Findings of Small Bowel Involvement of Amyloidosis Mimicking Small Bowel Polyposis Syndrome: a Case Report
0
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Amyloidosis is an all-inclusive disease of deposition of amyloid proteins in the extracellular spaces, which in localized or systemic form cause tissue damage and dysfunction. Herein, we report a case of small bowel involvement of systemic amyloidosis presenting with multiple polypoid wall thickening mimicking small bowel polyposis syndrome in an age 75 male. Interestingly, polypoid wall thickening and amyloidoma showed hypointensity on T2-weighted images. To our knowledge, there has been no literature describing MRI findings of poylpoid wall thickening and amyloidoma. Although the underlying mechanisms are unclear and need validation, hypointensity on T2-weighted images could be valuable in diagnosing small bowel involvement of amyloidosis in patients presenting with poylpoid wall thickening and amyloidoma.
Abstract
Amyloidosis is an all-inclusive disease of deposition of amyloid proteins in the extracellular spaces, which in localized or systemic form cause tissue damage and dysfunction. Herein, we report a case of small bowel involvement of systemic amyloidosis presenting with multiple polypoid wall thickening mimicking small bowel polyposis syndrome in an age 75 male. Interestingly, polypoid wall thickening and amyloidoma showed hypointensity on T2-weighted images. To our knowledge, there has been no literature describing MRI findings of poylpoid wall thickening and amyloidoma. Although the underlying mechanisms are unclear and need validation, hypointensity on T2-weighted images could be valuable in diagnosing small bowel involvement of amyloidosis in patients presenting with poylpoid wall thickening and amyloidoma.
참고문헌 (9)
- Benson MD, "Amyloid nomenclature 2018 : recommendations by the International Society of Amyloidosis(ISA)nomenclature committee", Amyloid, 25, pp.215~219 (2018)
- Kim SH, "Abdominal amyloidosis : spectrum of radiological findings", Clin Radiol, 58, pp.610~620 (2003)
- Mainenti PP, "Intestinal amyloidosis : two cases with different patterns of clinical and imaging presentation", World J Gastroenterol, 16, pp.2566~2570 (2010)
- Ozcan HN, "Imaging for abdominal involvement in amyloidosis", Diagn Interv Radiol, 23, pp.282~285 (2017)
- Saindane AM, "Focal amyloidoma of the small bowel mimicking adenocarcinoma on CT", AJR Am J Roentgenol, 185, pp.1187~1189 (2005)
- Rajkumar SV, "Monoclonal gammopathy of undetermined significance, Waldenstrom macroglobulinemia, AL amyloidosis, and related plasma cell disorders: diagnosis and treatment", Mayo Clin Proc, 81, pp.693~703 (2006)
- Georgiades CS, "Amyloidosis : review and CT manifestations", Radiographics, 24, pp.405~416 (2004)
- Tada S, "Gastrointestinal amyloidosis : radiologic features by chemical types", Radiology, 190, pp.37~42 (1994)
- Gillmore JD, "Pathophysiology and treatment of systemic amyloidosis", Nat Rev Nephrol, 9, pp.574~586 (2013)