Lymphocytic interstitial pneumonia in a patient with Sjögren’s syndrome
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Lymphocytic interstitial pneumonia (LIP) is a rare benign lymphoproliferative disorder characterized by diffuse infiltration of the pulmonary parenchymal interstitium by polyclonal lymphocytes and plasma cells. LIP has been associated with a variety of clinical conditions; such as connective tissue disorders and other immune system abnormalities. Treatment usually involves administration of corticosteroids and other immunosuppressants. We report on a 38-year-old female patient who complained of shortness of breath, dry mouth, and dry eyes for more than 1 month, and was positive for Raynaud’s phenomenon. Based on surgical biopsy, she was diagnosed as having LIP accompanied by Sjögren’s syndrome. The patient was treated with highdose steroids followed by maintenance therapy for approximately 2 years, and her condition improved.
Abstract
Lymphocytic interstitial pneumonia (LIP) is a rare benign lymphoproliferative disorder characterized by diffuse infiltration of the pulmonary parenchymal interstitium by polyclonal lymphocytes and plasma cells. LIP has been associated with a variety of clinical conditions; such as connective tissue disorders and other immune system abnormalities. Treatment usually involves administration of corticosteroids and other immunosuppressants. We report on a 38-year-old female patient who complained of shortness of breath, dry mouth, and dry eyes for more than 1 month, and was positive for Raynaud’s phenomenon. Based on surgical biopsy, she was diagnosed as having LIP accompanied by Sjögren’s syndrome. The patient was treated with highdose steroids followed by maintenance therapy for approximately 2 years, and her condition improved.
참고문헌 (10)
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