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비강내 국소 에스트로겐으로 치료한 유전성 출혈성모세혈관확장증 1예

A Case of Hereditary Hemorrhagic Telangiectasia Managed withIntranasal Topical Estrogen

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참고문헌

키워드

주제분류이비인후과학

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Abstract

Hereditary hemorrhagic telangiectasia is an autosomal dominant disorder affecting blood vessels of the skin, mucous membrane and viscera. It is characterized by a clinical triad of multiple telangiectasia, recurrent hemorrhages and familial occurrence. In 80% of patients, epistaxia is the first presenting symptom. It can have a massive impact on the quality of life of those affected. Otolaryngologists should be familiar with this disease because of its potential systemic complication. Recently, we have experienced a 69 year old female complaining of melena and recurrent epistaxis for 20 years. Epistaxis was successfully managed with topical estrogen ointment. (Korean J Otolaryngol 2006;49:447-50)

참고문헌 (18)

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