41세 여자 환자에서 발생한 사골동 점액낭종을 동반한 섬유 이형성증 1예
A Case Report of 41-Year-Old Female with Fibrous Dysplasia Combined with Ethmoid Mucocele
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Fibrous dysplasia (FD) is a non-malignant progressive condition, which replaces normal boneand marrow with fibrous tissue and woven bone. Sinus mucocele is a cystic, expansile, and destructivelesion that occurs as a result of obstruction of the sinus ostium secondary to inflammation,trauma, anatomical variation, previous sinus surgery, tumor or FD. Among them, FDcombined with mucocele has been rarely reported. Here we report the first case of FD combinedwith ethmoid mucocele. The patient underwent endoscopic debulking of FD and marsupializationof mucocele. The mucocele was successfully marsupialized, and the patient’ssymptoms were completely resolved. We propose a new hypothesis that nasal mucosa invaginatesinto FD and forms a mucocele. For the treatment of ethmoid FD combined with mucocele,we recommend an endoscopic transnasal approach for debulking and marsupialization.
Abstract
Fibrous dysplasia (FD) is a non-malignant progressive condition, which replaces normal boneand marrow with fibrous tissue and woven bone. Sinus mucocele is a cystic, expansile, and destructivelesion that occurs as a result of obstruction of the sinus ostium secondary to inflammation,trauma, anatomical variation, previous sinus surgery, tumor or FD. Among them, FDcombined with mucocele has been rarely reported. Here we report the first case of FD combinedwith ethmoid mucocele. The patient underwent endoscopic debulking of FD and marsupializationof mucocele. The mucocele was successfully marsupialized, and the patient’ssymptoms were completely resolved. We propose a new hypothesis that nasal mucosa invaginatesinto FD and forms a mucocele. For the treatment of ethmoid FD combined with mucocele,we recommend an endoscopic transnasal approach for debulking and marsupialization.
참고문헌 (12)
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