단백질 S 결핍증이 있는 환자에게서 연속적으로 발생한 양측 돌발성 감각신경성 난청과인공와우 이식 수술 후 성공적으로 양측 청력이 회복된 증례
A Case of Bilateral Sequential Sudden Sensorineural Hearing Loss in Protein S Deficiency and Successful Recovery of Hearing After Cochlear Implantation
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Bilateral sequential sudden sensorineural hearing loss (SSHL) is a rare and challenging clini-cal condition, but its association with protein S deficiency has received limited attention. Thispaper reports a case of bilateral sequential SSHL in a patient with protein S deficiency whounderwent cochlear implantation and achieved significant improvement in hearing. The pa-tient received high-dose systemic corticosteroids and anticoagulation therapy before the im-plantation, which had no significant effect. Cochlear implantation was then performed in theleft ear, and the patient showed significant improvement in speech understanding and overallhearing ability. A year later, the patient underwent surgery for the opposite ear with favorableoutcome. This case highlights the potential benefits of cochlear implantation in patients withbilateral sequential SSHL and protein S deficiency and emphasizes the importance of consid-ering cochlear implantation as a treatment option in such patients.
Abstract
Bilateral sequential sudden sensorineural hearing loss (SSHL) is a rare and challenging clini-cal condition, but its association with protein S deficiency has received limited attention. Thispaper reports a case of bilateral sequential SSHL in a patient with protein S deficiency whounderwent cochlear implantation and achieved significant improvement in hearing. The pa-tient received high-dose systemic corticosteroids and anticoagulation therapy before the im-plantation, which had no significant effect. Cochlear implantation was then performed in theleft ear, and the patient showed significant improvement in speech understanding and overallhearing ability. A year later, the patient underwent surgery for the opposite ear with favorableoutcome. This case highlights the potential benefits of cochlear implantation in patients withbilateral sequential SSHL and protein S deficiency and emphasizes the importance of consid-ering cochlear implantation as a treatment option in such patients.
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