외이도 종물로 처음 확인된 랑게르한스 세포 조직구증

Abstract

Langerhans cell histiocytosis (LCH) is a rare disorder that can affect various organ systems, including bone, skin, and the central nervous system. Although temporal bone involvement is uncommon, it may be the initial and isolated presentation, particularly in children. We present a case of a 2-year-old boy with persistent otorrhea and external auditory canal granulation tissue, initially misdiagnosed as chronic otitis externa. Imaging later revealed extensive temporal bone destruction, and biopsy confirmed LCH. This case underscores the importance of considering systemic diseases such as LCH in pediatric patients with atypical or unresponsive external ear lesions, and highlights the critical role of early imaging and tissue diagnosis in avoiding delays in appropriate management.