Juvenile Paget’s Disease with Paranasal Sinus Aplasia
0
조회
0
다운로드
0
인용
0
참고문헌
키워드
초록
Juvenile Paget’s disease (JPD) is a rare skeletal disorder that’s characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-monthold Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
Abstract
Juvenile Paget’s disease (JPD) is a rare skeletal disorder that’s characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-monthold Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
참고문헌 (11)
- Choremis C, "Osteitis deformans (Paget’s disease) in an 11-year-old", Helv Paediatr Acta, 13(2), pp.185~188 (1958)
- Woodhouse NJ, "Paget’s disease in a 5-year-old: acute response to human calcitonin", Br Med J, 4(5835), pp.267~269 (1972)
- Swoboda W, "Hyperostosis corticalis deformans juvenilis: unfamiliar generalized osteopathy in 2 siblings", Helv Paediatr Acta, 13(4), pp.292~312 (1958)
- Tuysuz B, "Calcitonin treatment in osteoectasia with hyperphosphatasia (juvenile Paget’s disease): radiographic changes after treatment", Pediatr Radiol, 29(11), pp.838~841 (1999)
- Whalen JP, "Calcitonin treatment in hereditary bone dysplasia with hyperphosphatasemia: a radiographic and histologic study of bone", AJR Am J Roentgenol, 129(1), pp.29~35 (1977)
- Thompson RC Jr, "Hereditary hyperphosphatasia. Studies of three siblings", Am J Med, 47(2), pp.209~219 (1969)
- Tehranzadeh J, "Computed tomography of Paget disease of the skull versus fibrous dysplasia", Skeletal Radiol, 27(12), pp.664~672 (1998)
- Eyring EJ, "Congenital hyperphosphatasia A clinical, pathological, and biochemical study of two cases", J Bone Joint Surg Am, 50(6), pp.1099~1117 (1968)
- Doyle FH, "Healing of the bones in juvenile Paget’s disease treated by human calcitonin", Br J Radiol, 47(553), pp.9~15 (1974)
- Cassinelli HR, "Familial idiopathic hyperphosphatasia (FIH): response to long-term treatment with pamidronate (APD)", Bone Miner, 19(2), pp.175~184 (1992)
- Spindler A, "Chronic idiopathic hyperphosphatasia. Report of a case treated with pamidronate and a review of the literature", J Rheumatol, 19(4), pp.642~645 (1992)