지방흡입술 이후 발생한 양측 상완 신경총 손상으로 나타난 압박마비유전신경병 - 증례보고
Hereditary Neuropathy with Liability to Pressure Palsies Presenting with Bilateral Brachial Plexopathy after Liposuction - Case Report
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Hereditary neuropathy with liability to pressure palsies (HNPP) is an autosomal dominant disorder characterized by recurrent entrapment neuropathies following an episode of compression or trauma. Reports on bilateral brachial plexopathy of HNPP are rare. We report on a case of a 21-year-old female patient with no past medical history, who presented with sudden paralysis and hypoesthesia of bilateral upper extremities after undergoing liposuction. Clinical and electrodiagnostic tests were consistent with brachial plexopathy. Genetic study for the peripheral myelin protein-22 (PMP22) gene confirmed the diagnosis of HNPP presenting with bilateral brachial plexopathy. This case indicates that HNPP should be suspected in patients with brachial plexopathy when it develops after pressure-leading events such as a minor surgical procedure.
Abstract
Hereditary neuropathy with liability to pressure palsies (HNPP) is an autosomal dominant disorder characterized by recurrent entrapment neuropathies following an episode of compression or trauma. Reports on bilateral brachial plexopathy of HNPP are rare. We report on a case of a 21-year-old female patient with no past medical history, who presented with sudden paralysis and hypoesthesia of bilateral upper extremities after undergoing liposuction. Clinical and electrodiagnostic tests were consistent with brachial plexopathy. Genetic study for the peripheral myelin protein-22 (PMP22) gene confirmed the diagnosis of HNPP presenting with bilateral brachial plexopathy. This case indicates that HNPP should be suspected in patients with brachial plexopathy when it develops after pressure-leading events such as a minor surgical procedure.
참고문헌 (10)
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